OBJECTIVES: Patients with Beckwith-Wiedemann syndrome (BWS) have a risk of 7.5% to
10% of developing childhood tumors, 60% of which are Wilms' tumors. Aberrant methylation …

Abstract “Genetic mosaicism” describes the presence of two or more populations of cells
within a single individual that differ in their genomic constitution. Although the occurrence of …

Abstract Beckwith–Wiedemann Syndrome (BWS) is an overgrowth syndrome caused by a
variety of molecular changes on chromosome 11p15. 5. Children with BWS have a …

Abstract The Beckwith–Wiedemann syndrome (BWS) is characterized by somatic
overgrowth and a predisposition to pediatric embryonal tumors. It is associated with genetic …

Beckwith–Wiedemann syndrome (BWS) is an overgrowth syndrome characterized by an
excessive prenatal and postnatal growth, macrosomia, macroglossia, and hemihyperplasia …

Beckwith–Wiedemann syndrome is an overgrowth disorder with an increased risk of
childhood tumors that results from a dysregulation of imprinted gene expression in the …

Genomic imprinting has been implicated in the aetiology of an overgrowth cancer-prone
syndrome, the Wiedemann-Beckwith syndrome (WBS). We have demonstrated uniparental …

Abstract Background Beckwith-Wiedemann syndrome (BWS) is a congenital overgrowth
disorder associated with abnormalities in 11p15. 5 imprinted genes. The most common …

Beckwith‐Wiedermann syndrome (BWS) comprises of a number of childhood abnormalities,
often associated with one or more tumors. Thirty‐eight patients were investigated to …

Beckwith-Wiedemann syndrome (BWS) is a congenital overgrowth syndrome associated
with a characteristic pattern of visceromegaly and predisposition to childhood tumours. BWS …