A cross-species analysis of the cystic fibrosis transmembrane conductance regulator. Potential functional domains and regulatory sites.

G Diamond, TF Scanlin, MA Zasloff… - Journal of Biological …, 1991 - ASBMB
To help elucidate the function of the cystic fibrosis transmembrane conductance regulator
(CFTR), we have undertaken a cross-species analysis of the DNA sequence which encodes …

Comparative genomic sequence analysis of the human and mouse cystic fibrosis transmembrane conductance regulator genes

RE Ellsworth, DC Jamison… - Proceedings of the …, 2000 - National Acad Sciences
The identification of the cystic fibrosis transmembrane conductance regulator gene (CFTR)
in 1989 represents a landmark accomplishment in human genetics. Since that time, there …

Cloning the mouse homolog of the human cystic fibrosis transmembrane conductance regulator gene

F Tata, P Stanier, C Wicking, S Halford, H Kruyer… - Genomics, 1991 - Elsevier
The cystic fibrosis transmembrane conductance regulator is encoded by the gene known to
be mutated in patients with cystic fibrosis. This paper reports the cloning and sequencing of …

Immunocytochemical analysis reveals differences between the subcellular localization of normal and ΔPhe508 recombinant cystic fibrosis transmembrane …

W Dalemans, J Hinnrasky, P Slos, D Dreyer… - Experimental cell …, 1992 - Elsevier
Cystic fibrosis (CF) is caused by mutations in the gene coding for the cystic fibrosis
transmembrane conductance regulator (CFTR). The most common mutation responsible for …

Multiple mutations in highly conserved residues are found in mildly affected cystic fibrosis patients

M Dean, MB White, J Amos, B Gerrard, C Stewart… - Cell, 1990 - cell.com
We have identified three different point mutations in the coding region of the cystic fibrosis
transmembrane conductance regulator (CFTR) gene. Each mutation segregates with the …

[HTML][HTML] Alternative splicing of intron 23 of the human cystic fibrosis transmembrane conductance regulator gene resulting in a novel exon and transcript coding for a …

K Yoshimura, CS Chu, RG Crystal - Journal of Biological Chemistry, 1993 - Elsevier
The cystic fibrosis transmembrane conductance regulator (CFTR) gene, the gene
responsible for the lethal hereditary disorder cystic fibrosis, codes for a membrane protein …

Expression and chromosome localization of the murine cystic fibrosis transmembrane conductance regulator

KA Kelley, S Stamm, CA Kozak - Genomics, 1992 - Elsevier
Abstract A 13.5-kb genomic fragment of the mouse cystic fibrosis transmembrane
conductance regulator (CFTR) gene was isolated from a C 57 BL 6 J liver DNA library, using …

[HTML][HTML] Partial purification of the cystic fibrosis transmembrane conductance regulator.

LS Ostedgaard, MJ Welsh - Journal of Biological Chemistry, 1992 - Elsevier
We have investigated several purification strategies for the cystic fibrosis transmembrane
regulator (CFTR) based on its structural similarity to other proteins of the traffic ATPase/ABC …

[HTML][HTML] Characterization of the promoter region of the cystic fibrosis transmembrane conductance regulator gene.

JL Chou, R Rozmahel, LC Tsui - Journal of Biological Chemistry, 1991 - Elsevier
To identify the transcription regulatory elements of the cystic fibrosis transmembrane
conductance regulator (CFTR) gene, DNA fragments located in the 5 '-upstream region were …

Molecular cloning and sequence analysis of the murine cDNA for the cystic fibrosis transmembrane conductance regulator

T Yorifuji, WK Lemna, CF Ballard, CL Rosenbloom… - Genomics, 1991 - Elsevier
We have cloned the mouse homolog of the human cystic fibrosis transmembrane
conductance regulator (CFTR) using clones isolated from a mouse lung cDNA library and …