Dissection in Marfan syndrome: the importance of the descending aorta

L Mimoun, D Detaint, D Hamroun, F Arnoult… - European heart …, 2011 - academic.oup.com
Aims To better characterize patients with Marfan syndrome who have survived an acute
aortic dissection and to estimate the risks of events in the descending aorta. Up until now …

Acute aortic dissection determines the fate of initially untreated aortic segments in Marfan syndrome

FS Schoenhoff, S Jungi, M Czerny, E Roost… - Circulation, 2013 - Am Heart Assoc
Background—The aim of the current study was to investigate incidence and causes of
surgical interventions in primarily nontreated aortic segments after previous aortic repair in …

[HTML][HTML] Aortic dissection in patients with Marfan syndrome based on the IRAD data

HWL de Beaufort, S Trimarchi, A Korach… - Annals of …, 2017 - ncbi.nlm.nih.gov
Abstract Between January 1996 and May 2017, the International Registry on Acute Aortic
Dissections has collected information on a total of 6,424 consecutive patients with acute …

Survival and complication free survival in Marfan's syndrome: implications of current guidelines

M Groenink, TAJ Lohuis, JGP Tijssen, MSJ Naeff… - Heart, 1999 - heart.bmj.com
OBJECTIVE To evaluate survival and complication free survival in patients with Marfan's
syndrome and to assess the possible influence of recently revised guidelines for …

Type A aortic dissection in Marfan syndrome: extent of initial surgery determines long-term outcome

B Rylski, JE Bavaria, F Beyersdorf, E Branchetti… - Circulation, 2014 - Am Heart Assoc
Background—Data on outcomes after Stanford type A aortic dissection in patients with
Marfan syndrome are limited. We investigated the primary surgery and long-term results in …

Surgical management of aortic dissection in patients with the Marfan syndrome.

JA Smith, JI Fann, DC Miller, KA Moore, A DeAnda Jr… - Circulation, 1994 - europepmc.org
Background Aortic dissection is one of the most lethal potential complications in patients
with the Marfan syndrome. Methods and results Among 360 patients undergoing operative …

Epidemiological profile of Marfan syndrome in a general population: a national database study

HH Chiu, MH Wu, HC Chen, FY Kao, SK Huang - Mayo Clinic Proceedings, 2014 - Elsevier
Objective To explore the current epidemiological profile of Marfan syndrome in a general
population. Patients and Methods Patients who had received a diagnosis of Marfan …

[HTML][HTML] Aortic diameter predicts acute type A aortic dissection in patients with Marfan syndrome but not in patients without Marfan syndrome

EK Kim, SH Choi, K Sung, WS Kim, YH Choe… - The Journal of thoracic …, 2014 - Elsevier
Objectives Among the parameters for surveillance of patients at risk of acute type A aortic
dissection, the aortic size has been considered a cardinal factor. Preventive surgery of the …

The risk for type B aortic dissection in Marfan syndrome

AW den Hartog, R Franken, AH Zwinderman… - Journal of the American …, 2015 - jacc.org
Background: Aortic dissections involving the descending aorta are a major clinical problem
in patients with Marfan syndrome. Objectives: The purpose of this study was to identify …

Aortic event rate in the Marfan population: a cohort study

G Jondeau, D Detaint, F Tubach, F Arnoult, O Milleron… - Circulation, 2012 - Am Heart Assoc
Background—Optimal management, including timing of surgery, remains debated in Marfan
syndrome because of a lack of data on aortic risk associated with this disease. Methods and …