1.6±2.6; P= 0.582). Native T1 relaxation times were prolonged in DM patients compared with
control subjects (1018.8±37.9 versus 970.3±29.9 ms; P< 0.0001). ECV measures were also …

BACKGROUND: Patients with myotonic muscular dystrophy (DM) are at risk for
atrioventricular block and left ventricular (LV) dysfunction. Noninvasive detection of diffuse …

Background—Myotonic dystrophy type 2 (DM2) is a genetic disorder characterized by
skeletal muscle symptoms, metabolic changes, and cardiac involvement. Histopathologic …

Background Conduction disease and arrhythmias represent a major cause of mortality in
myotonic muscular dystrophy type 1 (MMD1). Permanent pacemaker (PPM) implantation is …

In myotonic dystrophy type 2 (DM2/PROMM), cardiac muscle involvement is usually more
benign than in DM1, but clinically severe cardiomyopathy has been reported in some …

Background Myotonic dystrophy type 1 (MD1) is a neuromuscular disorder with potential
involvement of the heart and increased risk of sudden death. Considering the importance of …

Background The burden of cardiac disease in patients with muscular dystrophy (MD) is high
and includes cardiomyopathy, conduction abnormalities, and sudden cardiac death. This …

Background Cardiac involvement is a major determinant of prognosis in type 1 myotonic
dystrophy (DM1), but limited information is available about myocardial remodeling and …

Introduction: To evaluate myocardial strain and extracellular volume in myotonic dystrophy
type 1 (DM1) patients as potential imaging biomarkers of subclinical cardiac pathology …

Muscular dystrophies (MD) represent a heterogeneous group of rare genetic diseases that
often lead to significant weakness due to progressive muscle degeneration. In many forms of …