Short QT syndrome in pediatrics

R Pereira, O Campuzano, G Sarquella-Brugada… - Clinical Research in …, 2017 - Springer
Short QT syndrome is a malignant cardiac disease characterized by the presence of
ventricular tachyarrhythmias leading to syncope and sudden cardiac death. Currently …

The long QT syndrome: a transatlantic clinical approach to diagnosis and therapy

PJ Schwartz, MJ Ackerman - European heart journal, 2013 - academic.oup.com
The mind-boggling progress in the understanding of the molecular mechanisms underlying
the long QT syndrome (LQTS) has been the subject of many articles and reviews. Still, when …

Short QT syndrome

C Wolpert, E Schulze-Bahr - Clinical Cardiogenetics, 2020 - Springer
Short QT syndrome is a genetically transmitted disease caused by mutations in different
genes that is associated with atrial arrhythmias but more importantly with a severely …

The short QT syndrome

JC Hancox, MJ McPate, A El Harchi, AS Butler… - Heart Rate and Rhythm …, 2023 - Springer
The short QT syndrome (SQTS) is characterised by abbreviated QT intervals on the
electrocardiogram and by an increased risk of atrial and ventricular arrhythmias and of …

Congenital long QT syndrome: severe torsades de pointes provoked by epinephrine in a digenic mutation carrier

VH Tan, H Duff, V Kuriachan, B Gerull - Heart & Lung, 2014 - Elsevier
Abstract Congenital Long QT Syndrome (LQTS) is a potentially lethal cardiac channelopathy
characterized by prolongation of the corrected QT (QTc) interval on the surface …

Short QT syndrome in current clinical practice

S Khera, JT Jacobson - Cardiology in review, 2016 - journals.lww.com
Short QT syndrome is a rare inherited autosomal dominant cardiac channelopathy
associated with malignant ventricular and atrial arrhythmias. A shortened corrected QT …

Congenital long QT syndrome

MJ Ackerman, A Khositseth, DJ Tester… - Electrical Diseases of the …, 2008 - Springer
Once considered an extremely rare yet lethal arrhythmogenic peculiarity, congenital long QT
syndrome (LQTS) is understood today as a primary cardiac arrhythmia syndrome (“cardiac …

New insights into the long-QT syndrome

SG Priori, T Rossenbacker - Revista Espanola de Cardiologia, 2007 - iris.unipv.it
The long QT syndrome (LQTS) is an arrhythmogenic disease in which the prolongation of
cardiac repolarization alters the heart's electrical stability and predisposes affected …

Cardiac K+ channels and inherited long QT syndrome

MD Drici, J Barhanin - Pharmacology of Ionic Channel Function: Activators …, 2000 - Springer
The hallmark of all long QT syndromes (LQTS) is an abnormal ventricular repolarization
characterized by a prolonged QT interval on the electrocardiogram. LQTS have a drastically …

Long QT interval syndrome

NT Vatutin, EV Skliannaia, PV Gritsenko - Kardiologiia, 2002 - europepmc.org
Long QT interval syndrome is a cardiac disorder associated with fatal ventricular arrhythmias
(torsade de pointes and ventricular fibrillation). Timely diagnosis and adequate treatment …