Long QT interval syndrome

NT Vatutin, EV Skliannaia, PV Gritsenko - Kardiologiia, 2002 - europepmc.org
Long QT interval syndrome is a cardiac disorder associated with fatal ventricular arrhythmias
(torsade de pointes and ventricular fibrillation). Timely diagnosis and adequate treatment …

Congenital long QT syndrome: severe torsades de pointes provoked by epinephrine in a digenic mutation carrier

VH Tan, H Duff, V Kuriachan, B Gerull - Heart & Lung, 2014 - Elsevier
Abstract Congenital Long QT Syndrome (LQTS) is a potentially lethal cardiac channelopathy
characterized by prolongation of the corrected QT (QTc) interval on the surface …

Quinidine to treat short QT syndrome: a real alternative to ICD?

C Giustetto - Cardiac Arrhythmias 2005: Proceedings of the 9th …, 2006 - Springer
Short QT syndrome (SQTS) is a recently described familial arrhythmogenic disorder related
to an accelerated repolarisation time. Patients with short QT syndrome present with a wide …

Congenital long QT syndrome

MJ Ackerman, A Khositseth, DJ Tester… - Electrical Diseases of the …, 2008 - Springer
Once considered an extremely rare yet lethal arrhythmogenic peculiarity, congenital long QT
syndrome (LQTS) is understood today as a primary cardiac arrhythmia syndrome (“cardiac …

Short and long QT syndromes: does QT length really matter?

JP Couderc, CM Lopes - Journal of electrocardiology, 2010 - Elsevier
The short and long QT syndromes are inherited diseases associated with an increased risk
for life-threatening arrhythmias. The first case of long QT syndrome (LQTS) was reported …

The long QT syndrome

J Vohra - Heart, Lung and Circulation, 2007 - Elsevier
The long QT syndrome (LQTS) is a genetically transmitted cardiac arrhythmia due to ion
channel protein abnormalities, which affects the transport of potassium and sodium ions …

Congenital long QT syndrome

GM Vincent, K Timothy, L Zhang - Cardiac Electrophysiology Review, 2002 - Springer
The congenital Long QT syndrome (LQTS) is a primary electrophysiologic disorder of the
heart caused by mutations of genes which encode three different cardiac ion channels. The …

Long-term prognosis of short QT interval in Korean patients: a multicenter retrospective cohort study

DY Kim, JS Uhm, M Kim, IS Kim, MN Jin, HT Yu… - BMC Cardiovascular …, 2021 - Springer
Background Short QT syndrome is a rare, inherited channelopathy associated with sudden
cardiac arrest (SCA) but the characteristics and prognosis of short QT interval (SQTI) in …

Long QT syndrome: diagnosis and management

IA Khan - American heart journal, 2002 - Elsevier
Background Long QT syndrome (LQT) is characterized by prolongation of the QT interval,
causing torsade de pointes and sudden cardiac death. The LQT is a disorder of cardiac …

[HTML][HTML] Molecular pathogenesis of long QT syndrome type 1

J Wu, WG Ding, M Horie - Journal of arrhythmia, 2016 - Elsevier
Long QT syndrome type 1 (LQT1) is a subtype of a congenital cardiac syndrome caused by
mutation in the KCNQ1 gene, which encodes the α-subunit of the slow component of …