Introduction Hypertrophic cardiomyopathy (HCM) represents a generalized myopathic
process affecting both ventricular and atrial myocardium. Reduced left atrial (LA) function …

Aims To quantify the association between myotonic dystrophy (DM) and cardiac disease in a
nationwide cohort. Methods and results We identified a nationwide cohort of 1146 DM …

BACKGROUND: Myotonic dystrophy is associated with arrhythmias and risk of sudden
death but also with symptoms of heart failure. Our study aimed to identify early biventricular …

The aims of this study were to investigate the correlations of tri-nucleotide (CTG) repeat
length with detailed echocardiography (ECHO) parameters that represent myocardial …

INTRODUCTION AND OBJECTIVES: Myotonic dystrophy type 1 is characterized by muscle
damage and systemic manifestations, including cardiac involvement. Our aim was to …

Cardiac complications are the leading cause of death in patients with Duchenne muscular
dystrophy (DMD). Two-dimensional echocardiography is the current standard for monitoring …

AIMS: To estimate the degree of cardiac involvement regarding left ventricular ejection
fraction, conduction abnormalities, arrhythmia, risk of sudden cardiac death (SCD) and the …

Background Determination of myocardial deformation (strain) by two‐dimensional (2D)
speckle tracking echocardiography (STE) is a new method for evaluating left ventricular (LV) …

OBJECTIVE: The aim of the study was to identify, in addition to conduction defects, possible
predictors of cardiac events and death in patients with myotonic dystrophy (DM1) …

Background. Myocardial fibrosis occurs in the subepicardial myocardium of the left
ventricular posterior wall in patients with Duchenne Muscular Dystrophy (DMD). The aim of …