BACKGROUND: Patients with myotonic muscular dystrophy (DM) are at risk for
atrioventricular block and left ventricular (LV) dysfunction. Noninvasive detection of diffuse …

1.6±2.6; P= 0.582). Native T1 relaxation times were prolonged in DM patients compared with
control subjects (1018.8±37.9 versus 970.3±29.9 ms; P< 0.0001). ECV measures were also …

In myotonic dystrophy type 2 (DM2/PROMM), cardiac muscle involvement is usually more
benign than in DM1, but clinically severe cardiomyopathy has been reported in some …

Background Myotonic dystrophy type 1 (MD1) is a neuromuscular disorder with potential
involvement of the heart and increased risk of sudden death. Considering the importance of …

Objective Cardiac disease accounts for a large burden of premature mortality and morbidity
in patients with type 1 myotonic dystrophy (MD). However, little is known about structural …

Background—Myotonic dystrophy type 2 (DM2) is a genetic disorder characterized by
skeletal muscle symptoms, metabolic changes, and cardiac involvement. Histopathologic …

To assess subendocardial (long-axis) and mid-wall (short-axis) left ventricular (LV) function
in patients with type 1 myotonic dystrophy (MD1), with no symptoms or clinical signs of heart …

Background Myotonic dystrophy type 1 (DM1) is associated with increased cardiac morbidity
and mortality. Therefore, assessment of cardiac involvement and risk stratification for sudden …

Background Conduction disease and arrhythmias represent a major cause of mortality in
myotonic muscular dystrophy type 1 (MMD1). Permanent pacemaker (PPM) implantation is …

Introduction: To evaluate myocardial strain and extracellular volume in myotonic dystrophy
type 1 (DM1) patients as potential imaging biomarkers of subclinical cardiac pathology …