AIMS: To estimate the degree of cardiac involvement regarding left ventricular ejection
fraction, conduction abnormalities, arrhythmia, risk of sudden cardiac death (SCD) and the …

Background Patients with myotonic dystrophy type 1 (DM1) have a three-fold higher risk of
sudden cardiac death (SCD) than age-matched healthy controls. Despite numerous …

Myotonic dystrophy (DM) is an inherited disorder transmitted in an autosomal dominant
fashion and characterized by myotonia with dystrophic involvement of muscles and other …

Background Frequency and severity of cardiac involvement in DM2 are still controversial.
The aims of our study were to determine the frequency and progression of cardiac and …

BACKGROUND: Myotonic dystrophy type 1 (DM1) is a neurological disorder with known
cardiac involvement, including conduction disturbances, arrhythmias, and ventricular …

Objective Myotonic dystrophy type 1 (DM1) is the most frequent muscular dystrophy in
adults. DM1 is a multisystem disorder also affecting the heart with an increased incidence of …

BACKGROUND: Myotonic dystrophy type 1 (DM1) is a neurologic disorder with known
cardiac involvement, including left ventricular systolic dysfunction (LVSD), heart failure (HF) …

Aims To describe the incidence and identify predictors of sudden death (SD), major
conduction defects and sustained ventricular tachyarrhythmias (VTA) in myotonic dystrophy …

Objective Cardiac disease accounts for a large burden of premature mortality and morbidity
in patients with type 1 myotonic dystrophy (MD). However, little is known about structural …

Myotonic dystrophy (MD) is a multisystem, autosomal dominant disorder best known for its
skeletal muscle manifestations. Cardiac manifestations arise as a result of myocardial fatty …