[HTML][HTML] Loss of the Spinocerebellar Ataxia type 3 disease protein ATXN3 alters transcription of multiple signal transduction pathways

L Zeng, D Zhang, HS McLoughlin, AJ Zalon… - PLoS …, 2018 - journals.plos.org
Spinocerebellar ataxia type 3 (SCA3) is a dominantly inherited neurodegenerative disorder
caused by a polyglutamine-encoding CAG repeat expansion in the ATXN3 gene which …

Inactivation of the mouse Atxn3 (ataxin-3) gene increases protein ubiquitination

I Schmitt, M Linden, H Khazneh, BO Evert… - Biochemical and …, 2007 - Elsevier
Spinocerebellar ataxia type 3 is a neurodegenerative disease caused by expansion of a
polyglutamine domain in the protein ataxin-3 (ATXN3). Physiological functions of ATXN3 …

[HTML][HTML] Partial loss of ataxin-1 function contributes to transcriptional dysregulation in spinocerebellar ataxia type 1 pathogenesis

J Crespo-Barreto, JD Fryer, CA Shaw, HT Orr… - PLoS …, 2010 - journals.plos.org
Spinocerebellar ataxia type 1 (SCA1) is a dominantly inherited neurodegenerative disease
caused by expansion of a CAG repeat that encodes a polyglutamine tract in ATAXIN1 …

Comparison of spinocerebellar ataxia type 3 mouse models identifies early gain-of-function, cell-autonomous transcriptional changes in oligodendrocytes

B Ramani, B Panwar, LR Moore, B Wang… - Human molecular …, 2017 - academic.oup.com
Abstract Spinocerebellar ataxia type 3 (SCA3) is a neurodegenerative disorder caused by a
polyglutamine-encoding CAG repeat expansion in the ATXN3 gene. This expansion leads to …

Spinocerebellar ataxia type 1: Molecular mechanisms of neurodegeneration and preclinical studies

JM Pérez Ortiz, HT Orr - Polyglutamine Disorders, 2018 - Springer
Abstract Spinocerebellar ataxia type 1 (SCA1) is an adult-onset, inherited disease that leads
to degeneration of Purkinje cells of the cerebellum and culminates in death 10–30 years …

[HTML][HTML] Mutant ataxin1 disrupts cerebellar development in spinocerebellar ataxia type 1

CR Edamakanti, J Do, A Didonna… - The Journal of …, 2018 - Am Soc Clin Investig
Spinocerebellar ataxia type 1 (SCA1) is an adult-onset neurodegenerative disease caused
by a polyglutamine expansion in the protein ATXN1, which is involved in transcriptional …

Impaired oligodendrocyte maturation is an early feature in SCA3 disease pathogenesis

KH Schuster, AJ Zalon, H Zhang… - Journal of …, 2022 - Soc Neuroscience
Spinocerebellar ataxia Type 3 (SCA3), the most common dominantly inherited ataxia, is a
polyglutamine neurodegenerative disease for which there is no disease-modifying therapy …

[HTML][HTML] Ubiquitin-binding site 1 of pathogenic ataxin-3 regulates its toxicity in Drosophila models of Spinocerebellar Ataxia Type 3

MV Prifti, K Libohova, AL Harris, WL Tsou… - Frontiers in …, 2023 - frontiersin.org
Spinocerebellar Ataxia Type 3 (SCA3) is a member of the family of polyglutamine (polyQ)
diseases that are caused by anomalous CAG triplet repeat expansions in several genes …

Phosphorylation of ATXN1 at Ser776 in the cerebellum

ND Jorgensen, JM Andresen, S Lagalwar… - Journal of …, 2009 - Wiley Online Library
Abstract Spinocerebellar ataxia type 1 (SCA1) is one of nine inherited neurodegenerative
disorders caused by a mutant protein with an expanded polyglutamine tract …

Gene co-expression network analysis for identifying modules and functionally enriched pathways in SCA2

LT Pflieger, W Dansithong, S Paul… - Human molecular …, 2017 - academic.oup.com
Abstract Spinocerebellar ataxia type 2 (SCA2) is an autosomal dominant neurodegenerative
disease caused by CAG repeat expansion in the ATXN2 gene. The repeat resides in an …