MLL-AF4 spreading identifies binding sites that are distinct from super-enhancers and that govern sensitivity to DOT1L inhibition in leukemia

J Kerry, L Godfrey, E Repapi, M Tapia, NP Blackledge… - Cell Reports, 2017 - cell.com
Understanding the underlying molecular mechanisms of defined cancers is crucial for
effective personalized therapies. Translocations of the mixed-lineage leukemia (MLL) gene …

Degree of recruitment of DOT1L to MLL-AF9 defines level of H3K79 Di-and tri-methylation on target genes and transformation potential

A Kuntimaddi, NJ Achille, J Thorpe, AA Lokken… - Cell reports, 2015 - cell.com
The MLL gene is a common target of chromosomal translocations found in human leukemia.
MLL-fusion leukemia has a consistently poor outcome. One of the most common …

Elucidating the importance of DOT1L recruitment in MLL-AF9 leukemia and hematopoiesis

SM Grigsby, A Friedman, J Chase, B Waas, J Ropa… - Cancers, 2021 - mdpi.com
Simple Summary MLL-rearranged leukemia, driven by MLL-fusion proteins, is an
aggressive, therapy-resistant leukemia found in> 60% of infant leukemia and~ 10% of adult …

MLL:: AF9 degradation induces rapid changes in transcriptional elongation and subsequent loss of an active chromatin landscape

SN Olsen, L Godfrey, JP Healy, YA Choi, Y Kai… - Molecular cell, 2022 - cell.com
MLL rearrangements produce fusion oncoproteins that drive leukemia development, but the
direct effects of MLL-fusion inactivation remain poorly defined. We designed models with …

DOT1L, the H3K79 methyltransferase, is required for MLL-AF9–mediated leukemogenesis

AT Nguyen, O Taranova, J He… - Blood, The Journal of the …, 2011 - ashpublications.org
Chromosomal translocations of the mixed lineage leukemia (MLL) gene are a common
cause of acute leukemias. The oncogenic function of MLL fusion proteins is, in part …

DOT1L inhibition reveals a distinct subset of enhancers dependent on H3K79 methylation

L Godfrey, NT Crump, R Thorne, IJ Lau… - Nature …, 2019 - nature.com
Enhancer elements are a key regulatory feature of many important genes. Several general
features including the presence of specific histone modifications are used to demarcate …

Aberrant chromatin at genes encoding stem cell regulators in human mixed-lineage leukemia

MG Guenther, LN Lawton, T Rozovskaia… - Genes & …, 2008 - genesdev.cshlp.org
Mixed-lineage leukemia (MLL) fusion proteins are potent inducers of leukemia, but how
these proteins generate aberrant gene expression programs is poorly understood. Here we …

A higher-order configuration of the heterodimeric DOT1L–AF10 coiled-coil domains potentiates their leukemogenenic activity

X Song, L Yang, M Wang, Y Gu, B Ye… - Proceedings of the …, 2019 - National Acad Sciences
Chromosomal translocations of MLL1 (Mixed Lineage Leukemia 1) yield oncogenic chimeric
proteins containing the N-terminal portion of MLL1 fused with distinct partners. The MLL1 …

Complementary activities of DOT1L and Menin inhibitors in MLL-rearranged leukemia

C Dafflon, VJ Craig, H Mereau, J Gräsel… - Leukemia, 2017 - nature.com
Chromosomal rearrangements of the mixed lineage leukemia (MLL/KMT2A) gene leading to
oncogenic MLL-fusion proteins occur in~ 10% of acute leukemias and are associated with …

Leukemic transformation by the MLL-AF6 fusion oncogene requires the H3K79 methyltransferase Dot1l

AJ Deshpande, L Chen, M Fazio… - Blood, The Journal …, 2013 - ashpublications.org
Abstract The t (6; 11)(q27; q23) is a recurrent chromosomal rearrangement that encodes the
MLLAF6 fusion oncoprotein and is observed in patients with diverse hematologic …