PURPOSE Adrenocortical carcinoma (ACC) is a rare aggressive pediatric malignancy with
distinct biology. Its treatment follows the principles developed for adults; pediatric-specific …

Purpose Adrenocortical carcinoma (ACC) is a rare tumor in children with important
distinctions from the adult disease. We reviewed the National Cancer Data Base (NCDB) to …

Adrenocortical cancer (ACC) in childhood is a rare disease with poor prognosis. Complete
surgical resection, systemic chemotherapy, and mitotane therapy are important curative …

BACKGROUND: Adrenocortical carcinoma (ACC) is rarely described in children. There is
variation in incidence worldwide. This study sought to identify national incidence rates and …

Pediatric adrenocortical carcinoma is a rare and potentially fatal disease. In contrast to tumor
in adults, most pediatric adrenocortical carcinomas are functional. Despite the dramatic …

Abstract Background/Aims: Adrenocortical carcinoma (ACC) is an aggressive childhood
cancer. Limited evidence exists on a definite histopathological criterion to differentiate ACC …

PURPOSE: This study reviews adrenocortical tumors in children to determine factors that
significantly affect outcome. METHODS: An institutional review board-approved …

Adrenocortical carcinoma (ACC) is a rare endocrine malignancy of the adrenal gland with
an unfavorable prognosis. It is rare in the pediatric population, with an incidence of 0.2-0.3 …

Objectives The aim of this retrospective international analysis was to evaluate the role of risk
factors in pediatric patients with adrenocortical carcinoma (ACC) observed in European …

Purpose We created a registry for pediatric adrenocortical tumors (ACTs), which are rare
and are not well characterized. We provide a descriptive analysis of 254 patients registered …