Abstract The Cerebellar Cognitive Affective/Schmahmann Syndrome (CCAS) manifests as
impaired executive control, linguistic processing, visual spatial function, and affect …

Background The cerebellar cognitive affective syndrome scale (CCAS-S) was recently
developed to detect specific neuropsychological deficits in patients with cerebellar diseases …

The cerebellar cognitive affective syndrome scale (CCAS-S) was designed to detect specific
cognitive dysfunctions in cerebellar patients but is scarcely validated in spinocerebellar …

Background Traditionally, cerebellar disorders including ataxias have been associated with
deficits in motor control and motor learning. Since the 1980's growing evidence has …

Highlights•Cognitive impairment in SCAs is well-established, but not universal in all
patients.•The CCAS Scale is the current standard for identifying cognitive impairments in …

Background Cognitive deficits were related to Spinocerebellar Ataxia type 3/Machado-
Joseph Disease (SCA3/MJD), but the Cerebellar Cognitive Affective Syndrome (CCAS) …

The role of the cerebellum in cognition, both in healthy subjects and in patients with
cerebellar diseases, is debated. Neuropsychological studies in spinocerebellar ataxia type 1 …

A subtype-specific impairment of cognitive functions in spinocerebellar ataxia (SCA) patients
is still debated. Thirty-two SCA patients (SCA1, 6; SC2, 3; SCA3, 15; SCA6, 8) and 14 …

Background The spinocerebellar ataxias (SCA) are a heterogeneous group of progressive
neurodegenerative disorders that are associated with diffuse cerebellar atrophy. While the …

Background A brief bedside test has recently been introduced by Hoche et al.(Brain, 2018)
to screen for the Cerebellar Cognitive Affective Syndrome (CCAS) in patients with cerebellar …