Cardiomyopathy, characterized by non-ischemic myocardial fibrosis of the left ventricle (LV)
with a myocarditis-like pattern, is a frequent cause of morbidity and mortality in patients with …

Cardiac magnetic resonance (CMR) is an established tool for risk stratification in several
cardiomyopathies, and its role in muscular dystrophies (MuD) looks promising. We sought to …

Introduction: Cardiomyopathy is a common complication in muscular dystrophy (MD)
patients, though the mechanism is not clear. Retrospective data from adults with Duchenne …

Patients with type 1 muscular dystrophy (MD1) exhibit a poor prognosis related to cardiac
involvement. Left Ventricular (LV) dysfunction with LVEF< 50% is strongly associated with …

Background Cardiomyopathy is a prominent feature of muscular dystrophies (MD) in adult
patients; however, the pathophysiology is not well understood. While LVH is the most …

Cardiac involvement in muscular dystrophy (MD) is known to cause heart failure (HF).
However, little is known about the differences in electrocardiographic and …

Objectives: This study sought to analyze whether cardiovascular magnetic resonance (CMR)
can detect and quantify myocardial damage in the early stages of cardiomyopathy in …

Background Abnormalities of dystrophin expression cause Duchenne Muscular Dystrophy
(D) or Becker Muscular Dystrophy (B). Since widespread use of non-invasive respiratory …

1.6±2.6; P= 0.582). Native T1 relaxation times were prolonged in DM patients compared with
control subjects (1018.8±37.9 versus 970.3±29.9 ms; P< 0.0001). ECV measures were also …

Background The burden of cardiac disease in patients with muscular dystrophy (MD) is high
and includes cardiomyopathy, conduction abnormalities, and sudden cardiac death. This …