Purpose To evaluate the potential of non-contrast myocardial T1 mapping on cardiovascular
magnetic resonance examination (CMR) in differentiating patients with Fabry disease (FD) …

Background—Fabry disease (FD) is an X-linked disorder of lysosomal metabolism affecting
multiple organs with cardiac disease being the leading cause of death. Current imaging …

Fabry disease (FD) causes myocardial native T1 lowering on cardiac magnetic resonance
(CMR), left ventricular hypertrophy (LVH), and late gadolinium enhancement (LGE). LVH is …

Background Cardiovascular magnetic resonance (CMR) derived native myocardial T1 is
decreased in patients with Fabry disease even before left ventricular hypertrophy (LVH) …

Background: Fabry disease (FD) is a rare and treatable X-linked lysosomal storage disorder.
Cardiac involvement determines outcomes; therefore, detecting early changes is important …

Background Fabry disease (FD) is a treatable cause of hypertrophic cardiomyopathy (HCM).
We aimed to determine the independent predictors of FD and to define a clinically useful …

Please see the Author Video associated with this article. OBJECTIVE. Cardiac involvement
is the leading cause of mortality in Fabry disease. Noninvasive markers of cardiac …

Abstract Background Cardiac hypertrophy in Fabry disease can be assessed using the left
ventricular mass index (LVMI) with either echocardiography (LVMI-ECHO) or magnetic …

OBJECTIVE. Fabry's disease may be difficult to differentiate from symmetric hypertrophic
cardiomyopathy. Our aim was to compare the myocardial location and distribution patterns …

Fabry disease (FD) is a rare genetic X-linked disorder that can impact multiple organs.
Cardiac involvement influences the prognosis of patients with FD, being one of the main …