We describe the case of a patient with long QT syndrome and recurrent ventricular
fibrillation, triggered by premature ventricular complexes (PVCs) with a left bundle branch …

Background A 19-year-old woman with an established diagnosis of long QT syndrome
(LQTS) 2 and underlying KCNH2-mutation was referred to our centre for recurrent …

Short QT syndrome (SQTS) is a very rare inherited arrhythmic disease that is associated with
sudden cardiac death (SCD) caused by ventricular tachyarrhythmias. Gussak and …

Patients with long QT syndrome can sometimes present with a ventricular fibrillation (VF)
storm. Catheter ablation of culprit premature ventricular complexes responsible for the …

The patient underwent a comprehensive electrophysiologic study under conscious sedation
with and without isoproterenol administration. Bipolar intracardiac electrograms were …

Congenital long QT syndrome (LQTS) is the most common inherited arrhythmia, fatal
arrhythmias are the main causes of sudden death, and often induced by the premature …

A 57-year-old woman showed frequent premature ventricular complexes (PVCs) originating
from the right ventricular outflow tract (RVOT), and some of the PVCs triggered polymorphic …

A 6-year-old female with congenital long QT syndrome (LQTS) presented to the hospital with
recurrent syncope. She had frequent episodes of Torsade de pointes (TdP) that occurred at …

Pseudo 2: 1 AV block when sinus intervals are shorter than the ventricular refractory period
has been reported with long QT syndrome (LQTS). We report the characteristics and …

BACKGROUND: LQTS may cause sudden cardiac death (SCD), but the mechanisms linking
gene mutations to ventricular fibrillation (VF) are unclear. OBJECTIVE: To determine …