Cystic fibrosis: what do patients know, and what else would they like to know?

A Hames, J Beesley, R Nelson - Respiratory medicine, 1991 - Elsevier
As the survival of patients with cystic fibrosis (CF) improves, it becomes increasingly
important to address such issues as employment, reproduction, and quality of life in …

Pulmonary function and quality of life in adults with cystic fibrosis

N Smirnova, J Lowers, MJ Magee, SC Auld, WR Hunt… - Lung, 2023 - Springer
Purpose People living with cystic fibrosis (CF) experience impaired quality of life, but the
extent to which pulmonary function is associated with quality of life in CF remains unclear …

Managed care and the cystic fibrosis patient

KS McCoy, D Stokes, M Dubroff… - Current Opinion in …, 1997 - journals.lww.com
Since the first published report of mortality in cystic fibrosis in 1969, the median survival
among cystic fibrosis patients has risen from 14 to 31 years. The reasons for this improved …

Disparities in mortality of hispanic patients with cystic fibrosis in the United States. A national and regional cohort study

J Rho, C Ahn, A Gao, GS Sawicki, A Keller… - American journal of …, 2018 - atsjournals.org
Rationale: Patients of Hispanic origin with cystic fibrosis (CF) are the largest growing
minority, representing 8.5% of patients with CF in the United States. No national survival …

[HTML][HTML] Measuring and improving respiratory outcomes in cystic fibrosis lung disease: opportunities and challenges to therapy

ET Zemanick, JK Harris, S Conway, MW Konstan… - Journal of Cystic …, 2010 - Elsevier
Cystic fibrosis (CF) is a life-shortening disease with significant morbidity. Despite overall
improvements in survival, patients with CF experience frequent pulmonary exacerbations …

Caregiver burden in cystic fibrosis: a systematic literature review

C Daly, P Ruane, K O'Reilly… - Therapeutic …, 2022 - journals.sagepub.com
Background: Cystic fibrosis (CF) affects more than 80,000 people worldwide, having a
considerable impact on the quality of life of patients and their caregivers, who assist patients …

Update: epidemiology of cystic fibrosis

WS Krimsky, HW Parker - Current opinion in pulmonary medicine, 2002 - journals.lww.com
The natural history of cystic fibrosis (CF) is an evolving phenomenon. As such, it is
continually being redefined as epidemiologic data is collected and processed and as …

[HTML][HTML] Understanding the costs of care for cystic fibrosis: an analysis by age and health state

K Van Gool, R Norman, MB Delatycki, J Hall, J Massie - Value in health, 2013 - Elsevier
Objectives Cystic fibrosis (CF) is an inherited disease that requires more intensive
treatments as the disease progresses. Recent medical advancements have improved …

Longitudinal trends in health-related quality of life in adults with cystic fibrosis

EJ Dill, R Dawson, DE Sellers, WM Robinson… - Chest, 2013 - Elsevier
Background Health-related quality-of-life (HRQOL) measures have been used as patient-
reported outcomes in clinical trials in cystic fibrosis (CF), but there are limited data on …

Disparities in cystic fibrosis survival in Mexico: impact of socioeconomic status

AE Bustamante, LT Fernández, LC Rivas… - Pediatric …, 2021 - Wiley Online Library
Background Median survival age in cystic fibrosis (CF) has increased in developed
countries. Scarce literature exists about survival in Latin America, especially in Mexico. The …