Accelerated sinus rhythm prevents catecholaminergic polymorphic ventricular tachycardia in mice and in patients

M Faggioni, HS Hwang, C van der Werf… - Circulation …, 2013 - Am Heart Assoc
Rationale: Catecholaminergic polymorphic ventricular tachycardia (CPVT) is caused by
mutations in cardiac ryanodine receptor (RyR2) or calsequestrin (Casq2) genes. Sinoatrial …

Prevention of ventricular arrhythmia and calcium dysregulation in a catecholaminergic polymorphic ventricular tachycardia mouse model carrying calsequestrin‐2 …

R Alcalai, H Wakimoto, M Arad, D Planer… - Journal of …, 2011 - Wiley Online Library
Arrhythmia Prevention in CPVT. Background: Catecholaminergic polymorphic ventricular
tachycardia (CPVT) is a familial arrhythmic syndrome caused by mutations in genes …

Atropine-induced sinus tachycardia protects against exercise-induced ventricular arrhythmias in patients with catecholaminergic polymorphic ventricular tachycardia

PJ Kannankeril, MB Shoemaker, KA Gayle… - EP …, 2020 - academic.oup.com
Aims Catecholaminergic polymorphic ventricular tachycardia (CPVT) is an inherited
arrhythmia syndrome characterized by exercise-induced ventricular arrhythmias, sudden …

[HTML][HTML] Atrial arrhythmogenesis in catecholaminergic polymorphic ventricular tachycardia–is there a mechanistic link between sarcoplasmic reticulum Ca2+ leak and …

J Heijman, XHT Wehrens, D Dobrev - Acta physiologica (Oxford …, 2013 - ncbi.nlm.nih.gov
Catecholaminergic polymorphic ventricular tachycardia (CPVT) is caused by mutations in
the genes encoding the cardiac ryanodine receptor channel (RyR2) or the major …

Calmodulin kinase II inhibition prevents arrhythmias in RyR2R4496C+/− mice with catecholaminergic polymorphic ventricular tachycardia

N Liu, Y Ruan, M Denegri, T Bachetti, Y Li… - Journal of molecular and …, 2011 - Elsevier
Catecholaminergic polymorphic ventricular tachycardia (CPVT) is an inherited
arrhythmogenic disease characterized by life-threatening arrhythmias elicited by adrenergic …

[HTML][HTML] Arrhythmia initiation in catecholaminergic polymorphic ventricular tachycardia type 1 depends on both heart rate and sympathetic stimulation

TK Danielsen, R Manotheepan, M Sadredini, IS Leren… - PLoS …, 2018 - journals.plos.org
Aims Catecholaminergic polymorphic ventricular tachycardia type 1 (CPVT1) predisposes to
ventricular tachyarrhythmias (VTs) during high heart rates due to physical or psychological …

Paradoxical Effect of Increased Diastolic Ca2+ Release and Decreased Sinoatrial Node Activity in a Mouse Model of Catecholaminergic Polymorphic Ventricular …

P Neco, AG Torrente, P Mesirca, E Zorio, N Liu… - Circulation, 2012 - Am Heart Assoc
Background—Catecholaminergic polymorphic ventricular tachycardia is characterized by
stress-triggered syncope and sudden death. Patients with catecholaminergic polymorphic …

Sinus node dysfunction in catecholaminergic polymorphic ventricular tachycardia: risk factor and potential therapeutic target?

M Faggioni, C van der Werf, BC Knollmann - Trends in cardiovascular …, 2014 - Elsevier
Catecholaminergic polymorphic ventricular tachycardia (CPVT) is an inherited heart rhythm
disorder characterized by the occurrence of potentially life-threatening polymorphic …

Molecular and electrophysiological bases of catecholaminergic polymorphic ventricular tachycardia

U Mohamed, C Napolitano… - Journal of cardiovascular …, 2007 - Wiley Online Library
Catecholaminergic polymorphic ventricular tachycardia (CPVT) is an inherited
arrhythmogenic disorder characterized by adrenergically mediated polymorphic ventricular …

Distinct mechanisms mediate pacemaker dysfunction associated with catecholaminergic polymorphic ventricular tachycardia mutations: insights from computational …

L Arbel-Ganon, JA Behar, AM Gómez… - Journal of molecular and …, 2020 - Elsevier
Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a stress-induced
ventricular arrhythmia associated with rhythm disturbance and impaired sinoatrial node cell …