Abstract Spinocerebellar ataxia type 3 (SCA3), the commonest dominantly inherited ataxia
worldwide, is characterized by disruption in the cerebellar-cerebral and striatal-cortical …

Introduction Cognitive impairment has now been recognised to be present in patients with
several of spinocerebellar ataxias (SCAs). Cognitive impairment in patients with …

Background The natural history of clinical symptoms in the spinocerebellar ataxias (SCA) s
has been well characterised. However there is little longitudinal data comparing cognitive …

A subtype-specific impairment of cognitive functions in spinocerebellar ataxia (SCA) patients
is still debated. Thirty-two SCA patients (SCA1, 6; SC2, 3; SCA3, 15; SCA6, 8) and 14 …

Previous studies demonstrated cognitive impairments in spinocerebellar ataxia type 3
(SCA3/MJD); however, there is no consensus about the cognitive domains affected and the …

Spinocerebellar ataxias (SCAs) are characterized by a heterogeneous set of clinical
manifestations. Our aims were to assess the neurological features of SCA3, and to describe …

Highlights•Cognitive impairment in SCAs is well-established, but not universal in all
patients.•The CCAS Scale is the current standard for identifying cognitive impairments in …

Several authors have recently reported a broad cognitive impairment in autosomal dominant
cerebellar ataxias (ADCAs) patients. However, only a few studies on neuropsychological …

Objective: The aim of this study was to evaluate cognitive impairment in patients with
spinocerebellar ataxia type 6 (SCA6) and to verify the role of cerebellar involvement in …

The role of the cerebellum in cognition, both in healthy subjects and in patients with
cerebellar diseases, is debated. Neuropsychological studies in spinocerebellar ataxia type 1 …