Myotonic dystrophy type 1 (DM1) is the most common muscular dystrophy in adults. Cardiac
involvement is reported in 80% of cases and includes conduction disturbances, arrhythmias …

Background Cardiac involvement represents a major cause of morbidity and mortality in
patients with myotonic dystrophy type 1 (DM1) and prevention of sudden cardiac death …

Background Patients with myotonic dystrophy type 1 (DM1) have a three-fold higher risk of
sudden cardiac death (SCD) than age-matched healthy controls. Despite numerous …

Background Frequency and severity of cardiac involvement in DM2 are still controversial.
The aims of our study were to determine the frequency and progression of cardiac and …

Objective Myotonic dystrophy type 1 (DM1) is the most frequent muscular dystrophy in
adults. DM1 is a multisystem disorder also affecting the heart with an increased incidence of …

Abstract Myotonic dystrophy type 2 (DM2) is a slowly progressive, autosomal-dominant
disease. This is a multisystemic disorder that affects the heart, which is one of the main …

AIMS: To estimate the degree of cardiac involvement regarding left ventricular ejection
fraction, conduction abnormalities, arrhythmia, risk of sudden cardiac death (SCD) and the …

Background Cardiac involvement is a major determinant of prognosis in type 1 myotonic
dystrophy (DM1), but limited information is available about myocardial remodeling and …

Cardiac involvement is recorded in about 80% of patients affected by myotonic dystrophy
type 1 (DM1). The prevalence of cardiac conduction abnormalities and arrhythmias has …

Introduction Myotonic dystrophy is a multisystem disease associated with cardiac
abnormalities that are responsible for high morbidity and mortality. It commonly affects …