Background Myotonic dystrophy type 1 (DM1) is associated with increased cardiac morbidity
and mortality. Therefore, assessment of cardiac involvement and risk stratification for sudden …

Background Myotonic dystrophy type 1 (MD1) is a neuromuscular disorder with potential
involvement of the heart and increased risk of sudden death. Considering the importance of …

Structural alterations of the myocardium, such as fibrosis and fatty infiltration, were observed
in post-mortem examinations in patients with myotonic dystrophy, a familial multisystem …

Background—Myotonic dystrophy type 2 (DM2) is a genetic disorder characterized by
skeletal muscle symptoms, metabolic changes, and cardiac involvement. Histopathologic …

Objective Cardiac disease accounts for a large burden of premature mortality and morbidity
in patients with type 1 myotonic dystrophy (MD). However, little is known about structural …

Introduction: To evaluate myocardial strain and extracellular volume in myotonic dystrophy
type 1 (DM1) patients as potential imaging biomarkers of subclinical cardiac pathology …

BACKGROUND: Patients with myotonic muscular dystrophy (DM) are at risk for
atrioventricular block and left ventricular (LV) dysfunction. Noninvasive detection of diffuse …

Background Patients with myotonic dystrophy type 1 (DM1) have a three-fold higher risk of
sudden cardiac death (SCD) than age-matched healthy controls. Despite numerous …

BACKGROUND: Myotonic dystrophy type 1 (DM1) is a neurological disorder with known
cardiac involvement, including conduction disturbances, arrhythmias, and ventricular …

Background Conduction disease and arrhythmias represent a major cause of mortality in
myotonic muscular dystrophy type 1 (MMD1). Permanent pacemaker (PPM) implantation is …