Aortic Dissection in Marfan Syndrome: Protect the Tube of Life

AC Braverman - Journal of the American College of Cardiology, 2023 - jacc.org
Despite 50 years of heightened awareness and advances in medical therapy and aortic
surgery, aortic dissection (AD) remains a major cause of morbidity and mortality in Marfan …

[HTML][HTML] Adult patients with Marfan syndrome and ascending aortic surgery

MY Desai, V Kalahasti, E Hutt Centeno, K Chen… - Journal of the American …, 2019 - jacc.org
In Marfan syndrome (MFS), life expectancy has significantly improved with surveillance
imaging and aortic root (AR) replacement (ARR)(composite valve aortic graft replacement …

Type B Aortic Dissection and Distal Aortic Repair in Patients With Marfan Syndrome

K Newhall, T Benyakorn, S Banning… - Journal of Vascular …, 2021 - jvascsurg.org
Objective Patients with Marfan syndrome (MFS) are at risk of type B aortic dissection (TBAD).
We measured the annual incidence of TBAD in individuals with MFS, defined their …

Acute aortic dissection determines the fate of initially untreated aortic segments in Marfan syndrome

FS Schoenhoff, S Jungi, M Czerny, E Roost… - Circulation, 2013 - Am Heart Assoc
Background—The aim of the current study was to investigate incidence and causes of
surgical interventions in primarily nontreated aortic segments after previous aortic repair in …

Comparison of aortic dissection in Korean patients with versus without the marfan syndrome

EK Kim, ER Choi, SM Ko, SY Jang, SH Choi… - The American journal of …, 2012 - Elsevier
Among the cardiovascular manifestations in the Marfan syndrome (MFS), aortic dissection
stands out as a major cause of early mortality. The aim of this study was to test the …

[HTML][HTML] Aortic dissection in patients with Marfan syndrome based on the IRAD data

HWL de Beaufort, S Trimarchi, A Korach… - Annals of …, 2017 - ncbi.nlm.nih.gov
Abstract Between January 1996 and May 2017, the International Registry on Acute Aortic
Dissections has collected information on a total of 6,424 consecutive patients with acute …

Type A aortic dissection in Marfan syndrome: extent of initial surgery determines long-term outcome

B Rylski, JE Bavaria, F Beyersdorf, E Branchetti… - Circulation, 2014 - Am Heart Assoc
Background—Data on outcomes after Stanford type A aortic dissection in patients with
Marfan syndrome are limited. We investigated the primary surgery and long-term results in …

Comparison of aortic dissection in patients with and without Marfan's syndrome (results from the International Registry of Aortic Dissection)

JL Januzzi, F Marayati, RH Mehta, JV Cooper… - The American journal of …, 2004 - Elsevier
Among 1,049 patients diagnosed with aortic dissection in a multinational registry, patients
with Marfan's syndrome were typically younger and had unique presentations. Despite their …

Dissection in Marfan syndrome: the importance of the descending aorta

L Mimoun, D Detaint, D Hamroun, F Arnoult… - European heart …, 2011 - academic.oup.com
Aims To better characterize patients with Marfan syndrome who have survived an acute
aortic dissection and to estimate the risks of events in the descending aorta. Up until now …

Risk of type B dissection in Marfan syndrome: the Cornell aortic Aneurysm Registry

N Narula, RB Devereux, E Arbustini, X Ma… - Journal of the American …, 2023 - jacc.org
Background With preventive aortic grafting decreasing the incidence of type A dissections in
Marfan syndrome (MFS), most dissections are now type B, for which risk factors remain …