[PDF][PDF] Hyperinsulinaemic hypoglycaemia: genetic mechanisms, diagnosis and management

Z Mohamed, VB Arya, K Hussain - Journal of clinical research …, 2012 - jag.journalagent.com
Hyperinsulinaemic hypoglycaemia (HH) is characterized by unregulated insulin secretion
from pancreatic β-cells. Untreated hypoglycaemia in infants can lead to seizures …

[PDF][PDF] The diagnosis and management of hyperinsulinaemic hypoglycaemia

K Roženková, M Güemes, P Shah… - Journal of clinical …, 2015 - jag.journalagent.com
Insulin secretion from pancreatic β-cells is tightly regulated to keep fasting blood glucose
concentrations within the normal range (3.5-5.5 mmol/L). Hyperinsulinaemic hypoglycaemia …

Advances in the diagnosis and management of hyperinsulinemic hypoglycemia

RR Kapoor, C James, K Hussain - Nature Clinical Practice …, 2009 - nature.com
Hyperinsulinemic hypoglycemia (HH) is a consequence of unregulated insulin secretion by
pancreatic β-cells and is a major cause of hypoglycemic brain injury and mental retardation …

Insights in congenital hyperinsulinism

K Hussain - Congenital Endocrinopathies, 2007 - karger.com
Congenital hyperinsulinism is characterized by the unregulated secretion of insulin from
pancreatic Β-cells. The inappropriate insulin secretion causes severe and persistent …

[PDF][PDF] Congenital hyperinsulinism: diagnosis and treatment update

H Demirbilek, K Hussain - Journal of clinical research in …, 2017 - jag.journalagent.com
Pancreatic β-cells are finely tuned to secrete insulin so that plasma glucose levels are
maintained within a narrow physiological range (3.5-5.5 mmol/L). Hyperinsulinaemic …

Hyperinsulinaemic hypoglycaemia: genetic mechanisms, diagnosis and management

S Senniappan, B Shanti, C James… - Journal of inherited …, 2012 - Springer
Hyperinsulinaemic hypoglycaemia (HH) is due to the unregulated secretion of insulin from
pancreatic β-cells. A rapid diagnosis and appropriate management of these patients is …

Perspective on the genetics and diagnosis of congenital hyperinsulinism disorders

CA Stanley - The Journal of Clinical Endocrinology & …, 2016 - academic.oup.com
Context: Congenital hyperinsulinism (HI) is the most common cause of hypoglycemia in
children. The risk of permanent brain injury in infants with HI continues to be as high as 25 …

Diagnosis and treatment of hyperinsulinaemic hypoglycaemia and its implications for paediatric endocrinology

H Demirbilek, SA Rahman, GG Buyukyilmaz… - International journal of …, 2017 - Springer
Glucose homeostasis requires appropriate and synchronous coordination of metabolic
events and hormonal activities to keep plasma glucose concentrations in a narrow range of …

Diagnosis and management of hyperinsulinaemic hypoglycaemia

S Galcheva, S Al-Khawaga, K Hussain - Best Practice & Research Clinical …, 2018 - Elsevier
Hyperinsulinaemic hypoglycaemia (HH) is a heterogeneous condition with dysregulated
insulin secretion which persists in the presence of low blood glucose levels. It is the most …

Monogenic hyperinsulinemic hypoglycemia: current insights into the pathogenesis and management

K Lord, DD De León - International journal of pediatric endocrinology, 2013 - Springer
Hyperinsulinism (HI) is the leading cause of persistent hypoglycemia in children, which if
unrecognized may lead to development delays and permanent neurologicdamage. Prompt …