Short‐term prophylaxis in hereditary angioedema due to deficiency of the C 1‐inhibitor–a long‐term survey

H Farkas, Z Zotter, D Csuka, E Szabó, Z Nébenfűhrer… - Allergy, 2012 - Wiley Online Library
Background Hereditary angioedema is a potentially life‐threatening disorder, because
edema occurring in the mucosa of the upper airways can lead to suffocation. The …

Short-term prophylactic use of C1-inhibitor concentrate in hereditary angioedema: findings from an international patient registry

M Magerl, M Frank, W Lumry, J Bernstein… - Annals of Allergy …, 2017 - annallergy.org
Although most hereditary angioedema (HAE) attacks appear to occur spontaneously, they
can be precipitated by emotional stressors or physical triggers, including invasive medical or …

Standard care impact on angioedema because of hereditary C1 inhibitor deficiency: a 21‐month prospective study in a cohort of 103 patients

A Zanichelli, R Vacchini, M Badini, V Penna, M Cicardi - Allergy, 2011 - Wiley Online Library
To cite this article: Zanichelli A, Vacchini R, Badini M, Penna V, Cicardi M. Standard care
impact on angioedema because of hereditary C1 inhibitor deficiency: a 21‐month …

Long-term prophylaxis therapy in patients with hereditary angioedema with C1 inhibitor deficiency

T Craig, P Busse, RG Gower, DT Johnston… - Annals of Allergy …, 2018 - Elsevier
Objective To review the criteria for long-term prophylaxis therapy in patients with hereditary
angioedema due to C1 inhibitor deficiency (C1-INH-HAE), describe how these criteria have …

Recombinant human C1 inhibitor for the prophylaxis of hereditary angioedema attacks: a pilot study

A Reshef, D Moldovan, K Obtulowicz, I Leibovich… - Allergy, 2013 - Wiley Online Library
Background Hereditary angioedema (HAE) is a disease characterized by recurrent tissue
swelling affecting various body locations. Recent literature shows that patients with frequent …

Triggers and short-term prophylaxis in patients with hereditary angioedema.

T Craig - Allergy & Asthma Proceedings, 2020 - search.ebscohost.com
Background: Hereditary angioedema (HAE) is a rare disease that affects 1 in 60,000;
however, despite being extremely rare, the severity of the disease can cause significant …

Hereditary angioedema with C1 inhibitor deficiency: delay in diagnosis in Europe

A Zanichelli, M Magerl, H Longhurst, V Fabien… - Allergy, Asthma & …, 2013 - Springer
Background Hereditary angioedema (HAE) is a rare, debilitating, and potentially life-
threatening disease characterized by recurrent edema attacks. Important advances in HAE …

Hereditary angioedema with C1 inhibitor deficiency: clinical presentation and quality of life of 193 French patients

L Bouillet, D Launay, O Fain, I Boccon-Gibod… - Annals of Allergy …, 2013 - Elsevier
Background Hereditary angioedema (HAE) is a rare and potentially life-threatening disease.
New specific treatments are available. Objective To identify patients' features and patients' …

The global registry for hereditary angioedema due to C1-inhibitor deficiency

A Zanichelli, H Farkas, L Bouillet, N Bara… - Clinical Reviews in …, 2021 - Springer
Hereditary angioedema (HAE) is a rare condition, mostly due to genetic deficiency of
complement C1 inhibitor (C1-INH). The rarity of HAE impedes extensive data collection and …

Current treatment options for hereditary angioedema due to C1 inhibitor deficiency

MA Wu, A Zanichelli, M Mansi… - Expert Opinion on …, 2016 - Taylor & Francis
Introduction: Hereditary angioedema (HAE) usually results from C1 inhibitor (C1-INH)
deficiency or dysfunction. It is a rare autosomal dominant disorder characterized by …