Pyoderma gangrenosum, acne, psoriasis, arthritis and suppurative hidradenitis (PAPASH)‐
syndrome: a new entity within the spectrum of autoinflammatory syndromes?-Garzorz-2016 …

Pyoderma gangrenosum, acne, and hidradenitis suppurativa syndrome is a rare
inflammatory disease characterized by pyoderma gangrenosum (PG), mild to severe facial …

Background The group of autoinflammatory syndromes associated with Pyoderma
gangrenosum, Acne, and Suppurative Hidradenitis are poorly defined and difficult to control …

Autoinflammatory syndromes associated with hidradenitis suppurativa (HS) and/or acne are
rare but potentially debilitating disorders if not diagnosed and treated correctly. They share a …

Open access under CC BY-NC-ND license. and membrane-bound TNF-alfa. TNF-alfa is a
proinflammatory cytokine with a pathogenetic role in several immune-mediated diseases …

BACKGROUND: PAPA syndrome is a recently identified hereditary autoinflammatory
syndrome clinically characterized by pyogenic arthritis, severe acne, and pyoderma …

Hidradenitis suppurativa (HS) is an autoinflammatory skin disorder of the terminal hair
follicle, manifesting with painful nodules, abscesses, draining tunnels, and hypertrophic …

The clinical triad of pyoderma gangrenosum (PG), acne and suppurative hidradenitis
(PASH) has recently been described as a new disease entity within the spectrum of …

Autoinflammatory syndromes are characterized by recurrent episodes of sterile inflammation
in the absence of circulating autoantibodies or autoreactive T cells. PASH syndrome is a …

In the last decade, new scientific findings significantly improved our understanding of the
molecular pathogenesis of autoinflammation and have resulted in the identification and …