Congenital long QT syndrome (LQTS) is the most common inherited arrhythmia, fatal
arrhythmias are the main causes of sudden death, and often induced by the premature …

Short QT syndrome (SQTS) is a very rare inherited arrhythmic disease that is associated with
sudden cardiac death (SCD) caused by ventricular tachyarrhythmias. Gussak and …

BACKGROUND: LQTS may cause sudden cardiac death (SCD), but the mechanisms linking
gene mutations to ventricular fibrillation (VF) are unclear. OBJECTIVE: To determine …

Objective: To evaluate the main triggers of recurrent cardiac events in patients with
symptomatic congenital long QT syndrome (cLQTS). Methods: In this retrospective case …

Long QT syndrome (LQTS) is a rare arrhythmogenic condition characterized by abnormally
long QT intervals on an electrocardiogram. The prevalence varies between 1 in 3000 and 1 …

Aims To examine the initiating mode of Torsade de Pointes (TdP) in patients with congenital
long QT syndrome (LQTS). Methods and results We evaluated 111 episodes of TdP …

A 6-year-old female with congenital long QT syndrome (LQTS) presented to the hospital with
recurrent syncope. She had frequent episodes of Torsade de pointes (TdP) that occurred at …

Patients with long QT syndrome can sometimes present with a ventricular fibrillation (VF)
storm. Catheter ablation of culprit premature ventricular complexes responsible for the …

OBJECTIVES.: We sought to describe the mode of onset of spontaneous torsade de pointes
in the congenital long QT syndrome. BACKGROUND.: Contemporary classifications of the …

A 16 year-old asymptomatic male was diagnosed with long QT syndrome (LQTS) at age 7
due to family history and an abnormal electrocardiogram. Genetic testing confirmed the …