[HTML][HTML] Congenital long QT syndrome: treatment

PJ Schwartz, MJ Ackerman, S Asirvatham - UpToDate. Waltham, MA …, 2022 - medilib.ir
INTRODUCTION—Long QT syndrome (LQTS) is a disorder of ventricular myocardial
repolarization characterized by a prolonged QT interval on the electrocardiogram …

[HTML][HTML] Torsades de pointes during Myringotomy in a child with congenital long QT syndrome: a case report

M Coleman, JR Imundo, D Cortez… - The American Journal …, 2020 - ncbi.nlm.nih.gov
Objective: Congenital defects/diseases Background: Long QT syndrome (LQTS) is an
arrhythmogenic heart condition that can be congenital or acquired. Prolonged ventricular …

Gene mutation analysis of a Chinese family of congenital long QT syndrome type three

RM Shi, AQ Ma, YM Zhang, C Yang… - Zhonghua er ke za …, 2009 - europepmc.org
Objective The congenital long QT syndrome (LQTs) is a hereditary disorder in which most
affected family members have delayed ventricular repolarization manifested on the …

[PDF][PDF] Clinical and genetic characteristics and course of congenital long QT syndrome in children: A nine-year single-center experience

Y Ergül, GT Şahin, HC Kafalı, E Öztürk… - Anatolian Journal of …, 2021 - jag.journalagent.com
Objective: Long QT syndrome (LQTS) is an inherited primary arrhythmia syndrome
associated with life-threatening ventricular arrhythmias and sudden death. This study aimed …

Congenital long QT syndrome: 50 years of electrophysiological research from cell to bedside

L Wang - Acta Cardiologica, 2003 - Taylor & Francis
Congenital long QT syndrome (LQTS) is a group of ion channel disorders of ventricular
myocytes due to genetic mutations. The main symptoms of LQTS are pre-syncopal or …

Successful parental use of an automated external defibrillator for an infant with long-QT syndrome

A Divekar, R Soni - Pediatrics, 2006 - publications.aap.org
Congenital long-QT syndrome with 2: 1 atrioventricular block presenting in the perinatal
period is rare, has a poor prognosis, and leads to high risk for lethal ventricular arrhythmic …

Clinical and genetic analysis of long QT syndrome in children from six families in Saudi Arabia: are they different?

ZA Bhuiyan, S Al-Shahrani, AS Al-Khadra… - Pediatric …, 2009 - Springer
Congenital long QT syndrome (LQTS) is an inherited cardiac arrhythmia disorder
characterized by prolongation of the QT interval; patients are predisposed to ventricular …

Congenital long-QT syndromes: who's at risk for sudden cardiac death?

CI Berul - Circulation, 2008 - Am Heart Assoc
The congenital long-QT syndromes (LQTS) were initially described approximately 50 years
ago. 1–3 The principal events are syncope, seizures, and ventricular tachycardia …

Short QT syndrome in a pediatric patient

J Villafane, ML Young, P Maury, C Wolpert… - Pediatric …, 2009 - Springer
Short QT syndrome (SQTS) is a recently described genetic syndrome characterized by
abnormally brisk ventricular repolarization. Similar to long QT syndrome, SQTS might result …

Congenital Long QT Syndrome: A Review of Genetic and Pathophysiologic Etiologies, Phenotypic Subtypes, and Clinical Management

M Pandit, C Finn, UA Tahir, WH Frishman - Cardiology in Review, 2023 - journals.lww.com
Abstract Congenital Long QT Syndrome (CLQTS) is the most common inherited arrhythmia.
The QT interval, which marks the duration of ventricular depolarization and repolarization in …