[HTML][HTML] Congenital long QT syndrome: Pathophysiology and genetics

MJ Ackerman, PJ Schwartz, S Asirvatham - UpToDate https://www …, 2019 - medilib.ir
INTRODUCTION—Long QT syndrome (LQTS) is a disorder of ventricular myocardial
repolarization characterized by a prolonged QT interval on the electrocardiogram …

Long QT syndrome: first and fatal events provoked by hemodialysis

RF Miller, MW Haley, L Littmann - Pacing and clinical …, 2003 - Wiley Online Library
MILLER, RF, et al.: Long QT Syndrome: First and Fatal Events Provoked by Hemodialysis.
Long QT syndrome (LQTS) involves both congenital and acquired predispositions toward …

[HTML][HTML] Left cardiac sympathectomy prevents exercise-induced QTc prolongation in congenital long QT syndrome

L Wang - Experimental & Clinical Cardiology, 2003 - ncbi.nlm.nih.gov
Congenital long QT syndrome (LQTS) is a group of ion channel disorders of ventricular
myocytes caused by mutations of genes that encode these ion channels. The main clinical …

Device therapy in the setting of long QT syndrome

T Rhodes, R Weiss - Cardiac Electrophysiology Clinics, 2015 - cardiacep.theclinics.com
A 31-year-old woman with congenital long QT syndrome (LQTS) underwent dual-chamber
ICD implantation at 21 years of age for recurrent syncope. Her corrected QT interval (QTc) …

The long QT syndrome in children. An international study of 287 patients.

A Garson Jr, M Dick 2nd, A Fournier, PC Gillette… - Circulation, 1993 - Am Heart Assoc
BACKGROUND The Pediatric Electrophysiology Society studied children with the long QT
syndrome (LQTS) to describe the features of LQTS in patients less than 21 years old, define …

Congenital long QT syndrome

MJ Ackerman, A Khositseth, DJ Tester… - Electrical Diseases of the …, 2008 - Springer
Once considered an extremely rare yet lethal arrhythmogenic peculiarity, congenital long QT
syndrome (LQTS) is understood today as a primary cardiac arrhythmia syndrome (“cardiac …

Clinical and electrocardiographic features of patients with congenital long QT syndrome

JH Kim, GB Nam, HK Kim, KS Rhee… - Korean Circulation …, 2002 - synapse.koreamed.org
Background and Objectives Congenital long QT syndrome (LQTS) is characterized by the
prolongation of the QT interval, frequent episodes of syncope and Torsades de Pointes …

Mechanism of ventricular arrhythmias in the long QT syndrome: on hermeneutics

N EL‐SHERIF - Journal of Cardiovascular Electrophysiology, 2001 - Wiley Online Library
VT Mechanisms in LQTS. Both the congenital and acquired long QT syndrome are due to
abnormalities (intrinsic and/or acquired) of the ionic currents underlying repolarization. The …

Mechanism of arrhythmogenicity of the short–long cardiac sequence that precedes ventricular tachyarrhythmias in the long QT syndrome

N El-Sherif, EB Caref, M Chinushi, M Restivo - Journal of the American …, 1999 - jacc.org
OBJECTIVES The purpose of this study was to investigate the electrophysiologic
mechanism (s) that underlie the transition of one or more short–long (SL) cardiac sequences …

Two Cases of 2: 1 Atrioventricular Block in Infants with Idiopathic Long QT Syndrome

IJ KIM, BJ KIM - Journal of the Korean Pediatric Society, 1999 - pesquisa.bvsalud.org
Idiopathic long QT syndrome (LQTS) is an important cause of syncope, seizures, serious
ventricular arrhythmias and sudden death in children. The abnormalities of AV conduction …