Background Congenital long QT syndrome (LQTS) is a cardiac channelopathy whereby
patients may either remain lifelong asymptomatic or be symptomatic with a presentation of …

Congenital long QT syndrome (LQTS) is a familial disorder characterized by ventricular
repolarization that makes carriers vulnerable to malignant ventricular tachycardia and …

Congenital long QT syndrome (LQTS) represents a disorder of myocardial repolarization
characterized by a prolongation of QTc interval on ECG, which can degenerate into fast …

The diagnosis of congenital long-QT syndrome (LQTS) in the relatives (nonprobands) of
index patients (probands) is increasing because of screening. This report documents the …

Primary cardiac arrhythmias are often caused by defects, predominantly in the genes
responsible for generation of cardiac electrical potential, ie, cardiac rhythm generation. Due …

OBJECTIVES: The purpose of this study was to evaluate retrospectively a single-center
experience with the use of ICDs in patients with long QT syndrome (LQTS) concerning …

The short QT syndrome is a new congenital entity associated with familial atrial fibrillation
and/or sudden death or syncope occurring in all age groups, even in newborns. The …

ICDs in Long QT Syndrome. The congenital familial long QT syndrome (LQTS) is
characterized by QT interval prolongation on ECG and potentially life‐threatening …

OBJECTIVE To determine the frequency and predictors of pause dependent torsade de
pointes among patients with the congenital long QT syndrome and spontaneous ventricular …

Mechanisms of Ventricular Arrhythmia in LQT2 Heart. Introduction: The aim of this study was
to clarify the ventricular tachyarrhythmia mechanism induced by the IKr‐blocking agent …