Objective To explore the current epidemiological profile of Marfan syndrome in a general
population. Patients and Methods Patients who had received a diagnosis of Marfan …

Background Marfan syndrome is associated with morbidity and mortality due to aortic
dilatation and dissection. Preventive aortic root replacement has been the standard …

OBJECTIVE To evaluate survival and complication free survival in patients with Marfan's
syndrome and to assess the possible influence of recently revised guidelines for …

Background Marfan syndrome is a genetic disorder with considerable morbidity and
mortality. Presently, clinicians use the 2010 revised Ghent nosology, which includes optional …

Marfan syndrome is a connective tissue disorder with a worldwide prevalence of 1 in 5,000,
without any racial predilection. Major cardiovascular manifestations of Marfan disease often …

Aims To better characterize patients with Marfan syndrome who have survived an acute
aortic dissection and to estimate the risks of events in the descending aorta. Up until now …

Background: Prevention of aortic dissection and sudden death in patients with Marfan
syndrome (MFS) requires accurate diagnosis. MFS is diagnosed by the Ghent criteria, which …

The Marfan syndrome (MFS) is strongly associated with aortic disease causing a high
prevalence of prophylactic aortic surgery, aortic dissection, and sudden death. The aim of …

Among 1,049 patients diagnosed with aortic dissection in a multinational registry, patients
with Marfan's syndrome were typically younger and had unique presentations. Despite their …

OBJECTIVES.: We attempted to determine whether a family history of severe cardiovascular
disease in patients with the Marfan syndrome is associated with increased aortic dilation or …