Myocardial inflammation in Duchenne Muscular Dystrophy as a precipitating factor for heart failure: a prospective study

S Mavrogeni, A Papavasiliou, K Spargias… - BMC neurology, 2010 - Springer
Abstract Background In patients with Duchenne Muscular Dystrophy (DMD), the absent or
diminished dystrophin leads to progressive skeletal muscle and heart failure. We evaluated …

Mapping the current evidence on the anesthetic management of adult patients with neuromuscular disorders—a scoping review

LR van den Bersselaar, M Gubbels, S Riazi… - Canadian Journal of …, 2022 - Springer
Purpose Patients with neuromuscular disorders (NMDs) are at increased risk of
perioperative complications. The objective of this scoping review was to examine emerging …

Prognostic indicators of neuromuscular disorders for palliative care referral

RSK Chang, YK Wong - Annals of palliative medicine, 2018 - apm.amegroups.org
Background: Most of the neuromuscular disorders (NMDs) have poor prognosis and lead to
various symptoms amendable to palliative care. However, the suitable time of referral is …

Ambulatory monitoring and arrhythmic outcomes in pediatric and adolescent patients with Duchenne muscular dystrophy

CR Villa, RJ Czosek, H Ahmed, PR Khoury… - Journal of the …, 2015 - Am Heart Assoc
Background Patients with Duchenne Muscular Dystrophy (DMD) develop cardiac fibrosis
and dilated cardiomyopathy. We described the frequency of significant Holter findings in …

Sudden cardiac death in nonischemic cardiomyopathy: Refining risk assessment

MM Zipse, WS Tzou - Journal of Cardiovascular …, 2017 - Wiley Online Library
Sudden cardiac death (SCD) risk assessment among patients with nonischemic
cardiomyopathy (NICM) has been has been less straightforward than for patients with …

A longitudinal cause-of-death analysis of patients with Duchenne muscular dystrophy

T Matsumura, T Saito, H Fujimura… - Rinsho shinkeigaku …, 2011 - europepmc.org
Mechanical ventilation (MV) and cardiac protective therapy have improved the prognosis
and quality of life of patients with Duchenne muscular dystrophy (DMD). To understand how …

Cardiac management in neuromuscular diseases

HD Allen, PT Thrush, TM Hoffman, KM Flanigan… - Physical medicine and …, 2012 - Elsevier
This article addresses the pathophysiology, diagnostic approaches, and therapeutic options
in the more common forms of muscular dystrophy, especially those seen in pediatric and …

Use of advanced heart failure therapies in Duchenne muscular dystrophy

CA Wittlieb-Weber, CR Villa, J Conway, MJ Bock… - Progress in pediatric …, 2019 - Elsevier
Background As survival and neuromuscular function in Duchenne Muscular Dystrophy
(DMD) improve with glucocorticoid therapy and respiratory advances, the proportion of …

Current practices in treating cardiomyopathy and heart failure in Duchenne muscular dystrophy (DMD): understanding care practices in order to optimize DMD heart …

C Villa, SR Auerbach, N Bansal, BF Birnbaum… - Pediatric …, 2022 - Springer
Cardiac disease has emerged as a leading cause of mortality in Duchenne muscular
dystrophy in the current era. This survey sought to identify the diagnostic and therapeutic …

The value of cardiac MRI versus echocardiography in the pre-operative assessment of patients with Duchenne muscular dystrophy

A Brunklaus, E Parish, F Muntoni, S Scuplak… - european journal of …, 2015 - Elsevier
Abstract Background/purpose Duchenne Mmuscular Ddystrophy (DMD) related
cardiomyopathy is associated with significant perioperative mortality. Cardiac MRI (CMR) …