The cerebellar cognitive affective syndrome scale reveals early neuropsychological deficits in SCA3 patients

RP Maas, S Killaars, BPC van de Warrenburg… - Journal of …, 2021 - Springer
Background The cerebellar cognitive affective syndrome scale (CCAS-S) was recently
developed to detect specific neuropsychological deficits in patients with cerebellar diseases …

Cognitive decline is closely associated with ataxia severity in spinocerebellar ataxia type 2: a validation study of the Schmahmann Syndrome Scale

R Rodríguez-Labrada, A Batista-Izquierdo… - The Cerebellum, 2022 - Springer
The cerebellar cognitive affective syndrome scale (CCAS-S) was designed to detect specific
cognitive dysfunctions in cerebellar patients but is scarcely validated in spinocerebellar …

The CCAS-scale in hereditary ataxias: helpful on the group level, particularly in SCA3, but limited in individual patients

A Thieme, J Faber, P Sulzer, K Reetz, I Dogan… - Journal of …, 2022 - Springer
Background A brief bedside test has recently been introduced by Hoche et al.(Brain, 2018)
to screen for the Cerebellar Cognitive Affective Syndrome (CCAS) in patients with cerebellar …

Validation of a German version of the Cerebellar Cognitive Affective/Schmahmann Syndrome Scale: preliminary version and study protocol

A Thieme, S Roeske, J Faber, P Sulzer… - … research and practice, 2020 - Springer
Background Traditionally, cerebellar disorders including ataxias have been associated with
deficits in motor control and motor learning. Since the 1980's growing evidence has …

Neuropsychological features of patients with spinocerebellar ataxia (SCA) types 1, 2, 3, and 6

I Klinke, M Minnerop, T Schmitz-Hübsch, M Hendriks… - The cerebellum, 2010 - Springer
A subtype-specific impairment of cognitive functions in spinocerebellar ataxia (SCA) patients
is still debated. Thirty-two SCA patients (SCA1, 6; SC2, 3; SCA3, 15; SCA6, 8) and 14 …

Cognitive impairment in cerebellar lesions: a logit model based on neuropsychological testing

E Bolceková, M Mojzeš, Q Van Tran, J Kukal… - Cerebellum & …, 2017 - Springer
Background Damage to the cerebellum may lead to motor dysfunctions, but also to the
neuropsychological deficits that comprise the Cerebellar Cognitive Affective Syndrome …

Longitudinal study of cognitive and psychiatric functions in spinocerebellar ataxia types 1 and 2

R Fancellu, D Paridi, C Tomasello, M Panzeri… - Journal of …, 2013 - Springer
The role of the cerebellum in cognition, both in healthy subjects and in patients with
cerebellar diseases, is debated. Neuropsychological studies in spinocerebellar ataxia type 1 …

A longitudinal investigation into cognition and disease progression in spinocerebellar ataxia types 1, 2, 3, 6, and 7

A Moriarty, A Cook, H Hunt, ME Adams… - Orphanet Journal of …, 2016 - Springer
Background The natural history of clinical symptoms in the spinocerebellar ataxias (SCA) s
has been well characterised. However there is little longitudinal data comparing cognitive …

Neurocognitive changes in spinocerebellar ataxia type 3: a systematic review with a narrative design

KH Yap, RPC Kessels, S Azmin, B van de Warrenburg… - The Cerebellum, 2022 - Springer
Abstract Spinocerebellar ataxia type 3 (SCA3), the commonest dominantly inherited ataxia
worldwide, is characterized by disruption in the cerebellar-cerebral and striatal-cortical …

Cognitive impairment in spinocerebellar ataxia type 12

A Agarwal, H Kaur, A Agarwal, A Nehra… - Parkinsonism & Related …, 2021 - Elsevier
Introduction Cognitive impairment has now been recognised to be present in patients with
several of spinocerebellar ataxias (SCAs). Cognitive impairment in patients with …