Cognitive impairment in spinocerebellar ataxia type 6

M Suenaga, Y Kawai, H Watanabe, N Atsuta… - Journal of Neurology …, 2008 - jnnp.bmj.com
Objective: The aim of this study was to evaluate cognitive impairment in patients with
spinocerebellar ataxia type 6 (SCA6) and to verify the role of cerebellar involvement in …

Cerebellar cognitive affective syndrome in Machado Joseph disease: core clinical features

P Braga-Neto, JL Pedroso, H Alessi, LA Dutra… - The Cerebellum, 2012 - Springer
The cerebellum is no longer considered a purely motor control device, and convincing
evidence has demonstrated its relationship to cognitive and emotional neural circuits. The …

Prefrontal hypoperfusion and cognitive dysfunction correlates in spinocerebellar ataxia type 6

Y Kawai, M Suenaga, H Watanabe, M Ito, K Kato… - Journal of the …, 2008 - Elsevier
OBJECTIVE: The aim of this study is to evaluate the correlation between brain perfusion and
cognitive dysfunction in spinocerebellar ataxia type 6 (SCA6) patients. METHODS: Thirteen …

Neuropsychological picture of 33 spinocerebellar ataxia cases

L Orsi, F D'Agata, P Caroppo, A Franco… - Journal of Clinical …, 2011 - Taylor & Francis
We administered a large battery of neuropsychological tests to an heterogeneous cohort of
genetically defined spinocerebellar ataxia (SCA) patients in order to assess their cognitive …

Discordance between patient-reported outcomes and physician-rated motor symptom severity in early-to-middle-stage spinocerebellar ataxia type 3

RP Maas, DJLG Schutter, BPC van de Warrenburg - The Cerebellum, 2021 - Springer
Assessment of patient-reported outcome measures (PROMs) in spinocerebellar ataxias
(SCAs) could provide valuable insights into self-perceived health status. Although they are …

Composite cerebellar functional severity score: validation of a quantitative score of cerebellar impairment

ST Du Montcel, P Charles, P Ribai, C Goizet… - Brain, 2008 - academic.oup.com
Reliable and easy to perform functional scales are a prerequisite for future therapeutic trials
in cerebellar ataxias. In order to assess the specificity of quantitative functional tests of …

Depressive mood is associated with ataxic and non-ataxic neurological dysfunction in SCA3 patients

JAM Saute, ACF da Silva, KC Donis, L Vedolin… - The Cerebellum, 2010 - Springer
We read with interest the article recently published in Cerebellum by Klinke et al., entitled
“Neuropsychological features of patients with spinocerebellar ataxia (SCA) types 1, 2, 3, and …

Nonmotor symptoms in patients with spinocerebellar ataxia type 10

A Moro, RP Munhoz, M Moscovich, WO Arruda… - The Cerebellum, 2017 - Springer
Nonmotor symptoms (NMS) have been described in several neurodegenerative diseases
but have not been systematically evaluated in spinocerebellar ataxia type 10 (SCA10). The …

Cognitive impairment in spinocerebellar ataxia type 8

A Lilja, P Hämäläinen, E Kaitaranta, R Rinne - Journal of the neurological …, 2005 - Elsevier
OBJECTIVES: Only a limited number of studies have investigated the cognitive
performances of spinocerebellar ataxia (SCA) patients. In none of the SCA8 studies have …

Cognitive findings in spinocerebellar ataxia type 2: relationship to genetic and clinical variables

F Le Pira, G Zappalà, R Saponara, E Domina… - Journal of the …, 2002 - Elsevier
Several authors have recently reported a broad cognitive impairment in autosomal dominant
cerebellar ataxias (ADCAs) patients. However, only a few studies on neuropsychological …