Abstract Introduction About 50% of Fabry disease (FD) patients develop cardiac
manifestation, also known as Fabry cardiomyopathy. Beside echocardiography, cardiac …

Background Cardiac involvement is a major contributor of morbidity and mortality in Fabry
disease (FD). Early detection and accurate evaluation of the disease progression is …

In the past few years, the wide application of cardiac magnetic resonance (CMR)
significantly changed the approach to the study of cardiac involvement in Fabry Disease …

Background Cardiac involvement is common and is the leading cause of mortality in Fabry
disease (FD). We explored the association between cardiovascular magnetic resonance …

Please see the Author Video associated with this article. OBJECTIVE. Cardiac involvement
is the leading cause of mortality in Fabry disease. Noninvasive markers of cardiac …

Abstract Funding Acknowledgements Type of funding sources: None. Background Staging
of Fabry disease (FD) cardiomyopathy uses multiparametric cardiac MRI. Advanced disease …

Purpose The accumulation of sphingolipids in Fabry's disease (FD) leads to left ventricular
(LV) hypertrophy and shortened T1 in cardiac magnetic resonance (CMR). Early detection of …

Fabry disease (FD) is a rare genetic X-linked disorder that can impact multiple organs.
Cardiac involvement influences the prognosis of patients with FD, being one of the main …

Background: Non-invasive diagnosis of disease stage in Fabry cardiomyopathy with
multimodality imaging is pivotal when deciding on the appropriate time to initiate enzyme …

Background: Cardiovascular disease is the most common cause of death among Fabry
disease patients, who carry significantly increased risk for heart failure and sudden cardiac …