BACKGROUND: Conduction disturbances and arrhythmias characterize the cardiac feature
of myotonic dystrophy type 1 (MD1), and a myocardial involvement has been suggested as …

Aims To quantify the association between myotonic dystrophy (DM) and cardiac disease in a
nationwide cohort. Methods and results We identified a nationwide cohort of 1146 DM …

Myotonic dystrophy is an autosomal dominant genetic disease of nucleotide expansion
resulting in neuromuscular disease with two distinct subtypes. There are significant systemic …

Left ventricular hypertrabeculation (LVHT, noncompaction, noncompaction) is an
increasingly recognized morphological abnormality of the left ventricular myocardium …

Background Type 1 myotonic dystrophy (DM1) is associated with a variety of cardiac
conduction abnormalities and the frequent need for permanent pacing. However, the role of …

Myotonic dystrophy type 1 (DM1), the most common muscular dystrophy affecting adults and
children, is a multi-systemic disorder affecting skeletal, cardiac, and smooth muscles as well …

Myotonic dystrophy type 1 (DM1) is the most common muscular dystrophy in adults. Cardiac
involvement is reported in 80% of cases and includes conduction disturbances, arrhythmias …

PURPOSE: To prospectively determine whether a relationship exists between magnetic
resonance (MR) imaging abnormalities of the right ventricle (RV) and intracardiac …

Background and aims Myotonic dystrophy type 1 (DM1) and type 2 (DM2) are dominant
inherited muscular dystrophies with multiple systemic involvement, often producing cardiac …

Myotonic dystrophy (MD) is characterized by myotonia and muscular dystrophy and cardiac
involvement with tachy-arrhythmia is rarely encountered. Wereport a case of MDcomplicated …