PURPOSE: To prospectively determine whether a relationship exists between magnetic
resonance (MR) imaging abnormalities of the right ventricle (RV) and intracardiac …

Structural alterations of the myocardium, such as fibrosis and fatty infiltration, were observed
in post-mortem examinations in patients with myotonic dystrophy, a familial multisystem …

BACKGROUND: Patients with myotonic muscular dystrophy (DM) are at risk for
atrioventricular block and left ventricular (LV) dysfunction. Noninvasive detection of diffuse …

We evaluated the progression of conduction system and myocardial disease in 17
asymptomatic myotonic dystrophy patients by clinical evaluation, electrocardiography, vector …

Myotonic dystrophy is an autosomal dominant disease affecting many organ systems,
including the heart. Abnormalities of the cardiac conduction system are a frequent and well …

Objective Cardiac disease accounts for a large burden of premature mortality and morbidity
in patients with type 1 myotonic dystrophy (MD). However, little is known about structural …

We performed signal-averaged electrocardiography and 24-h ambulatory
electrocardiographic monitoring in 53 patients with myotonic dystrophy to determine the …

Background—Myotonic dystrophy type 2 (DM2) is a genetic disorder characterized by
skeletal muscle symptoms, metabolic changes, and cardiac involvement. Histopathologic …

Myotonic dystrophy is frequently associated with functional and anatomic derangements in
the myocardium. Ten myotonic dystrophy patients (seven men and three women, ages …

We utilized Doppler echocardiography to characterize left ventricular diastolic function in 42
patients with myotonic dystrophy (mean age 37±12 years, 64% male) who had no symptoms …