Background Marfan syndrome is associated with morbidity and mortality due to aortic
dilatation and dissection. Preventive aortic root replacement has been the standard …

The Marfan syndrome (MFS) is strongly associated with aortic disease causing a high
prevalence of prophylactic aortic surgery, aortic dissection, and sudden death. The aim of …

Background The purpose of this study was to analyze the risk of aortic events (death,
dissection, or aortic rupture) associated with Marfan syndrome and decide on the optimal …

Background: Prevention of aortic dissection and sudden death in patients with Marfan
syndrome (MFS) requires accurate diagnosis. MFS is diagnosed by the Ghent criteria, which …

OBJECTIVE To evaluate survival and complication free survival in patients with Marfan's
syndrome and to assess the possible influence of recently revised guidelines for …

OBJECTIVES The aim of this study was to explore sex and gender differences regarding
aortic events in Marfan patients. METHODS We analysed all data from our connective tissue …

Objective To explore the current epidemiological profile of Marfan syndrome in a general
population. Patients and Methods Patients who had received a diagnosis of Marfan …

Background—Optimal management, including timing of surgery, remains debated in Marfan
syndrome because of a lack of data on aortic risk associated with this disease. Methods and …

Background Aortic branch aneurysms are not included in the diagnostic criteria for Marfan
syndrome (MFS); however, their prevalence and eventual prognostic significance are …

Aims To better characterize patients with Marfan syndrome who have survived an acute
aortic dissection and to estimate the risks of events in the descending aorta. Up until now …