Pulmonary arterial hypertension (PAH) and other pulmonary vascular diseases remain a
source of great morbidity and mortality because they complicate several primary lung …

2 Circ Genom Precis Med. 2018; 11: e002317. DOI: 10.1161/CIRCGEN. 118.002317
December 2018 normal population of 6.0. None of the 7 PAH patients with the RNF213 p …

Case report A 50 year old woman was referred to Tufts Medical Center for evaluation of
Pulmonary Hypertension. She was born in New York City but relocated to Barbados as a …

Introduction Extrapulmonary manifestations of pulmonary arterial hypertension (PAH) may
play a critical pathobiological role and a deeper understanding will advance insight into …

Pulmonary arterial hypertension (PAH) is a progressive condition that is characterised by
inflammation, remodelling and progressive luminal narrowing in the pulmonary vasculature …

Pulmonary arterial hypertension (PAH) is a rare disease of the pulmonary vasculature
characterized by progressive vascular obliteration, right heart failure, and ultimately death …

IntroductionPulmonary arterial hypertension (PAH) associated with congenital heart disease
(CHD-PAH) is commonly caused by uncorrected left-to-right shunts at the atrial or ventricular …

Pulmonary arterial hypertension (PAH) is a relatively rare but potentially life-threatening
disease. In most forms, the disease is likely to be diagnosed late and is associated with …

Pulmonary arterial hypertension (PAH) has a complex pathobiology. The hallmark of PAH is
a distinctive obliterative remodelling of the pulmonary vasculature that involves all cell …

Pulmonary arterial hypertension (PAH) is a rare disease of the pulmonary vasculature
characterised by progressive remodelling and narrowing of the pulmonary arteries due to …