Congenital long-QT syndromes: who's at risk for sudden cardiac death?

CI Berul - Circulation, 2008 - Am Heart Assoc
The congenital long-QT syndromes (LQTS) were initially described approximately 50 years
ago. 1–3 The principal events are syncope, seizures, and ventricular tachycardia …

Congenital long QT syndrome

DJ Tester, PJ Schwartz, MJ Ackerman - … Diseases of the Heart: Volume 1 …, 2013 - Springer
With an incidence as high as 1 in 2,000–2,500 live births, long QT syndrome (LQTS) is often
characterized clinically by prolongation of the heart rate corrected QT interval (QTc) on a 12 …

Congenital long QT syndrome: diagnosis and management in pediatric patients

Y Bar-Cohen, MJ Silka - Current Treatment Options in Cardiovascular …, 2006 - Springer
Opinion statement The long QT syndrome (LQTS) is characterized by electrocardiographic
abnormalities and a high incidence of syncope and sudden cardiac death (SCD). The …

Clinical implications for patients with long QT syndrome who experience a cardiac event during infancy

C Spazzolini, J Mullally, AJ Moss, PJ Schwartz… - Journal of the American …, 2009 - jacc.org
Objectives: This study was designed to evaluate the clinical and prognostic aspects of long
QT syndrome (LQTS)-related cardiac events that occur in the first year of life (infancy) …

[PDF][PDF] Congenital long QT syndrome: considerations for primary care physicians

AJ Moss, JP Daubert - Clevel Clin J Med, 2008 - academia.edu
Congenital long QT syndrome is an inherited disorder of cardiac repolarization that
predisposes to syncope and to sudden death from polymorphic ventricular tachycardia. The …

Congenital long QT syndrome: Epidemiology and clinical manifestations

PJ Schwartz, MJ Ackerman… - U: UpToDate, Triedman JK …, 2018 - uptodate.com
Long QT syndrome (LQTS) is a disorder of ventricular myocardial repolarization
characterized by a prolonged QT interval on the electrocardiogram (ECG)(waveform 1) that …

Congenital long QT syndrome

MJ Ackerman, A Khositseth, DJ Tester… - Electrical Diseases of the …, 2008 - Springer
Once considered an extremely rare yet lethal arrhythmogenic peculiarity, congenital long QT
syndrome (LQTS) is understood today as a primary cardiac arrhythmia syndrome (“cardiac …

[HTML][HTML] QT interval duration remains a major risk factor in long QT syndrome patients

ET Locati - Journal of the American College of Cardiology, 2006 - jacc.org
Almost 50 years after the first description of congenital long QT syndrome (LQTS), where QT
interval prolongation was recognized as the hallmark of a new pathologic entity associated …

Diagnostic evaluation of long QT syndrome

W Shimizu - Cardiac electrophysiology clinics, 2012 - cardiacep.theclinics.com
Congenital long QT syndrome (LQTS) is one of the heritable channelopathies, characterized
by prolongation of QT interval in the standard 12-lead electrocardiogram (ECG) and a …

Short QT: when does it matter?

MN Viswanathan, RL Page - Circulation, 2007 - Am Heart Assoc
For half a century, the relationship between the QT interval and cardiac arrhythmias has
been recognized, 1 although attention has focused primarily on prolongation of the QT. The …