H cart involvement in myotonic dystrophy, the most common form of muscular dystrophy in
adult life,'is frequently found and has been extensively investigated. 2T3 Myocardial imp …

Myotonic dystrophy is frequently associated with functional and anatomic derangements in
the myocardium. Ten myotonic dystrophy patients (seven men and three women, ages …

A 37 year old man who presented with a cardiomyopathy, conduction defects and atrial and
ventricular arrhythmias was found to have the neuromuscular manifestations of myotonic …

We evaluated the progression of conduction system and myocardial disease in 17
asymptomatic myotonic dystrophy patients by clinical evaluation, electrocardiography, vector …

Thirty-eight consecutive adult patients with myotonic dystrophy were included in a study with
electrocardiography at rest and 24-hour ambulatory electrocardiography. The patients were …

Myotonic dystrophy is an autosomal dominant disease affecting many organ systems,
including the heart. Abnormalities of the cardiac conduction system are a frequent and well …

Eight young adult male patients with myotonic dystrophy, mean age 26 years, underwent 24-
hour Holter electrocardiographic monitoring and intracardiac electrophysiologic study. Right …

Myotonic muscular dystrophy (MyD) is the most common muscular dystrophy of adults. It
takes its name from myotonia, a prolonged contraction of voluntary muscle which diminishes …

In 12 autopsy cases of myotonic dystrophy, the most frequently observed histopathologic
lesions of the cardiac conduction system were fibrosis, fatty infiltration and atrophy. Fibrosis …

• Study of 30 patients with myotonic dystrophy and 17 unaffected family members in a total of
18 families by echocardiography and ECG, including noninvasive His-bundle recording …