Introduction: Idiopathic pulmonary fibrosis (IPF), the most common of the idiopathic
interstitial pneumonias, is a disease with a poor prognosis, and a highly heterogeneous and …

Idiopathic pulmonary fibrosis (IPF) is a chronic and progressive fibrotic disease limited to the
lung, with high variability in the course of disease from one patient to another. Patients with …

Background: AE-IPF is a deadly complication of IPF, for which no international guidelines
exist, resulting in global variability in prevention, diagnosis and treatment strategies …

Recognising recent advances, the definition and diagnostic criteria for acute exacerbation of
idiopathic pulmonary fibrosis (AE-IPF) have been updated by an international working …

Acute exacerbations of idiopathic pulmonary fibrosis (AE-IPF), with an annual incidence up
to 20% and a short-term mortality around 50%, are the more frequent cause of death in …

The goal of this review is to summarise the clinical features, management, and prognosis of
acute exacerbations of idiopathic pulmonary fibrosis (AE-IPF). AE-IPF has previously been …

Objective Few prospective cohort studies with relatively large numbers of patients with non-
idiopathic pulmonary fibrosis (non-IPF) of idiopathic interstitial pneumonia (IIP) have been …

Acute exacerbation of idiopathic pulmonary fibrosis (AE-IPF) is an often deadly complication
of IPF. No focussed international guidelines for the management of AE-IPF exist. The aim of …

Acute exacerbation is a major cause of morbidity and mortality in patients with idiopathic
pulmonary fibrosis. Although the real nature of it is still not clear and there is no proven …

Acute exacerbation of idiopathic pulmonary fibrosis (AE-IPF) is a clinical entity defined by
rapid deterioration of IPF during the course of the disease that is not due to infections …