Infantile epileptic encephalopathy with hypsarrhythmia (infantile spasms/West syndrome)
RA Hrachovy, JD Frost Jr - Journal of clinical neurophysiology, 2003 - journals.lww.com
Infantile spasms is a unique disorder peculiar to infancy and early childhood. In this article,
the clinical manifestations and electroencephalographic features of the disorder are …
the clinical manifestations and electroencephalographic features of the disorder are …
Symptomatology of infantile spasms
K Watanabe, T Negoro, A Okumura - Brain and Development, 2001 - Elsevier
Epileptic spasms in West syndrome consist of a brief phasic contraction followed by a
gradually relaxing tonic component, associated with typical ictal electroencephalographic …
gradually relaxing tonic component, associated with typical ictal electroencephalographic …
Infantile spasms syndrome, West syndrome and related phenotypes: what we know in 2013
P Pavone, P Striano, R Falsaperla, L Pavone… - Brain and …, 2014 - Elsevier
The current spectrum of disorders associated to clinical spasms with onset in infancy is
wider than previously thought; accordingly, its terminology has changed. Nowadays, the …
wider than previously thought; accordingly, its terminology has changed. Nowadays, the …
West syndrome: a comprehensive review
P Pavone, A Polizzi, SD Marino, G Corsello… - Neurological …, 2020 - Springer
Since its first clinical description (on his son) by William James West (1793–1848) in 1841,
and the definition of the classical triad of (1) infantile spasms;(2) hypsarrhythmia, and (3) …
and the definition of the classical triad of (1) infantile spasms;(2) hypsarrhythmia, and (3) …
A proposal for case definitions and outcome measures in studies of infantile spasms and West syndrome: consensus statement of the West Delphi group
AL Lux, JP Osborne - Epilepsia, 2004 - Wiley Online Library
Purpose: To reach a broad consensus on case definitions, outcomes, and outcome
measures that will ease future study design and facilitate comparison of data from different …
measures that will ease future study design and facilitate comparison of data from different …
Neurophysiology of spasms
F Vigevano, L Fusco, C Pachatz - Brain and Development, 2001 - Elsevier
Spasms are a form of epileptic seizure typical of infancy. From a clinical point of view, the
child presents a flexor–extensor movement involving the trunk and limbs and lasting about …
child presents a flexor–extensor movement involving the trunk and limbs and lasting about …
Infantile spasms in remission may reemerge as intractable epileptic spasms
P Camfield, C Camfield, A Lortie, H Darwish - Epilepsia, 2003 - Wiley Online Library
Background: West syndrome consists of infantile spasms with hypsarrhythmia and is
perceived as a disorder of infants. Methods: We describe 10 patients with West syndrome …
perceived as a disorder of infants. Methods: We describe 10 patients with West syndrome …
Epileptic spasms in clusters without hypsarrhythmia in infancy
RH Caraballo, N Fejerman, BD Bernardina… - Epileptic …, 2003 - Wiley Online Library
Spasms are defined as epileptic seizures characterized by brief axial contraction, in flexion,
extension or mixed, symmetric or asymmetric, lasting from a fraction of a second to 1‐2s, and …
extension or mixed, symmetric or asymmetric, lasting from a fraction of a second to 1‐2s, and …
Different neuronal networks are associated with spikes and slow activity in hypsarrhythmia
M Siniatchkin, A Van Baalen, J Jacobs, F Moeller… - …, 2007 - Wiley Online Library
Purpose: West syndrome is a severe epileptic encephalopathy of infancy characterized by a
poor developmental outcome and hypsarrhythmia. The pathogenesis of hypsarrhythmia is …
poor developmental outcome and hypsarrhythmia. The pathogenesis of hypsarrhythmia is …
What is West syndrome?
O Dulac - Brain and Development, 2001 - Elsevier
The combination of axial spasms in clusters, hypsarrhythmia, and psychomotor delay
beginning in the first year of life defines West syndrome. Variants of this classical triad …
beginning in the first year of life defines West syndrome. Variants of this classical triad …