Dilation of peripheral vessels in Marfan syndrome: importance of thoracoabdominal MR angiography

EM Mariucci, L Lovato, M Rosati, LM Palena… - International journal of …, 2013 - Elsevier
Objectives Aim of this study was to assess vascular morphology and dimension of the entire
aorta and branch vessels in MFS using thoracoabdominal MR angiography (MRA) …

[HTML][HTML] The fate of nonaortic arterial segments in Marfan patients

FS Schoenhoff, M Yildiz, B Langhammer… - The Journal of thoracic …, 2019 - Elsevier
Objectives The aim of this study was to investigate the fate of nonaortic arterial segments in
patients with Marfan syndrome (MFS). Methods This was a retrospective analysis of 100 …

Progressive pulmonary artery dilatation is associated with type B aortic dissection in patients with Marfan syndrome

C Brouwer, H Bulut, W van Gemert, AHJ Staal… - Journal of Clinical …, 2019 - mdpi.com
Objective: Marfan syndrome (MFS) is a connective tissue disorder associated with severe
cardiovascular morbidity and mortality. It is unknown if aorta complications in MFS are …

Thoracoabdominal aorta in Marfan syndrome: MR imaging findings of progression of vasculopathy after surgical repair.

S Kawamoto, DA Bluemke, TA Traill, EA Zerhouni - Radiology, 1997 - pubs.rsna.org
PURPOSE: To determine the natural history of vasculopathy of the thoracoabdominal aorta
in patients with Marfan syndrome after composite graft repair of the aortic root. MATERIALS …

Aortic distensibility in Marfan syndrome: a potential predictor of aortic events?

MM van Andel, V de Waard, J Timmermans… - Open …, 2021 - openheart.bmj.com
Objectives Patients with Marfan syndrome (MFS) are prone to develop aortic aneurysms due
to fragmentation of elastic fibres, resulting in reduced distensibility of the aorta. Reduced …

Cardiovascular pathology in Marfan syndrome—An overview

AE Becker - Cardiovascular aspects of Marfan syndrome, 1995 - Springer
The clinical presentation of arachnodactyly, better known as Marfan syndrome, has been
recognized for almost 100 years, but it is only relatively recent that McKusick (4) described …

1039 Prevalence of cardiovascular manifestations in patients with Marfan syndrome: a cardiovascular magnetic resonance study

F Alpendurada, R Mohiaddin - Journal of Cardiovascular Magnetic …, 2008 - Elsevier
Methods The study population consisted of 120 consecutive Marfan patients referred to our
centre between January 2003 and June 2007 including 77 males (64%) and 43 females …

Beyond the root: dilatation of the distal aorta in Marfan's syndrome

PM Engelfriet, E Boersma, JGP Tijssen, BJ Bouma… - Heart, 2006 - heart.bmj.com
Objective: To investigate dilatory changes of the aorta distal to the root in patients with
Marfan's syndrome. Methods and results: Data of 268 patients with Marfan's syndrome who …

Magnetic resonance angiography derived predictors of progressive dilatation and surgery of the aortic root in Marfan syndrome

JM Weinrich, A Lenz, G Schön, C Behzadi, I Molwitz… - Plos one, 2022 - journals.plos.org
Background To identify magnetic resonance (MR) angiography derived predictors of
progressive dilatation and surgery of the aortic root in Marfan syndrome. Material and …

Aortic stiffness and diameter predict progressive aortic dilatation in patients with Marfan syndrome

GJ Nollen, M Groenink, JGP Tijssen… - European heart …, 2004 - academic.oup.com
Abstract Aim Patients with Marfan syndrome may develop dissection due to progressive
dilatation in the entire aorta, which is not always predictable by mere anatomic assessment …