The aim of this prospective noninvasive follow-up study was (1) to assess the progression of
cardiac involvement (CI) in patients with myotonic dystrophy (MD), Becker's muscular …

BACKGROUND: Little is known about the long-term development and outcome of cardiac
involvement (CI) in patients with myotonic dystrophy type 1 (MD), Becker muscular dystrophy …

Objective To assess the progression of cardiac involvement (CI), defined as'
definite','possible'or'absent', based on history, clinical examination, electrocardiography, 24 …

The aim of this prospective study was to classify cardiac involvement in myopathies by
means of a comprehensive cardiac investigation, to determine the rate of cardiac …

Myotonic dystrophy is an autosomal dominant genetic disease of nucleotide expansion
resulting in neuromuscular disease with two distinct subtypes. There are significant systemic …

Abstract Myotonic dystrophy type 2 (DM2) is a slowly progressive, autosomal-dominant
disease. This is a multisystemic disorder that affects the heart, which is one of the main …

OBJECTIVE: The aim of the study was to identify, in addition to conduction defects, possible
predictors of cardiac events and death in patients with myotonic dystrophy (DM1) …

We evaluated the progression of conduction system and myocardial disease in 17
asymptomatic myotonic dystrophy patients by clinical evaluation, electrocardiography, vector …

Background Patients with myotonic dystrophy type 1 (DM1) have a three-fold higher risk of
sudden cardiac death (SCD) than age-matched healthy controls. Despite numerous …

Background Cardiac involvement is commonly present in various neuromuscular diseases
which may develop life-threatening consequences. The early manifestation is often …