… significance (45), this is not a rare scenario in the evaluation of a patient with suspected
ATTRwt amyloidosis. We recommend mass spectrometry as the preferred method for …

… that forms amyloid fibrils … amyloidosis is determined by the amyloid-forming protein and
the organ predilection. This review will focus on transthyretin amyloidosis, a form of amyloidosis …

… Peripheral neuropathy is the major clinical manifestation of transthyretin amyloidosis‘. This
… neuropathy does not occur in all patients with transthyretin amyloidosis and, indeed, many of …

… Studies referred to in this connection included a study documenting the risk of false
positive immunostaining for TTR amyloid in patients with AL amyloidosis, 142 and studies …

… For patients with systemic ATTR amyloidosis, TTR amyloid detection and characterisation
in one anatomical site is sufficient to make the diagnosis [ I, C]. A positive bone scintigraphy (…

… The liver is the primary source of systemic transthyretin protein. Liver transplantation has …
hereditary transthyretin amyloidosis, but continued deposition of wild-type transthyretin amyloid …

… transthyretin amyloidosis is the most frequent form of ATTR-CM found in the elderly, hereditary
transthyretin amyloidosis (… among elderly ATTR-CM patients, identify predictors of ATTRv …

… In conclusion, in patients with heart failure due to transthyretin amyloid cardiomyopathy, …
that tafamidis is an effective therapy for patients with transthyretin amyloid cardiomyopathy. …

… patients with hereditary TTR amyloidosis, 67 symptomatic patients with wild-type TTR
amyloidosis, and 274 currently asymptomatic individuals with a TTR mutation. Nineteen countries …

… variants of TTR (mutant transthyretin amyloidosis [ATTRm]; … is diagnostic of transthyretin
amyloidosis with predominant … in a patient with cardiac transthyretin amyloidosis at baseline. …