Hyper IgM syndrome: a report from the USIDNET registry

EA Leven, P Maffucci, HD Ochs, PR Scholl… - Journal of clinical …, 2016 - Springer
… -consented USIDNET Registry is … the Registry [21]. De-identified data available for research
purposes were used for the current study, for which a query was submitted to the USIDNET

The importance of primary immune deficiency registries: The united states immunodeficiency network registry

JP Lopes… - … and Allergy Clinics, 2020 - immunology.theclinics.com
… Using the registry data, the IDF and the USIDNET registry … by data from the USIDNET
registry and how these data have … X-linked hyper IgM syndrome with recombinant CD40 ligand. …

Rheumatologic diseases in patients with inborn errors of immunity in the USIDNET registry

N Padem, H Wright, R Fuleihan, E Garabedian… - Clinical …, 2022 - Springer
… cohort had 339 severe combined immunodeficiency (SCID), 92 non-specific combined
immunodeficiency (CID), and 156 hyper IgM syndrome (HIGM) patients. Among those, 1 SCID (…

Risk factors of pneumonia in primary antibody deficiency patients receiving immunoglobulin therapy: data from the US immunodeficiency network (USIDNET)

MN Syed, C Kutac, JM Miller, R Marsh… - Journal of Clinical …, 2022 - Springer
… The main strengths of this study include the use of USIDNET registry data, its large size, and
prospective data collection from thirty-nine institutions, and the broad representation of PAD …

Lymphoproliferative disease in CVID: a report of types and frequencies from a US patient registry

E Yakaboski, RL Fuleihan, KE Sullivan… - Journal of clinical …, 2020 - Springer
… For this study, the USIDNET registry was queried for lymphoproliferative disease as well as
… Sullivan contributed a significant portion of the CVID patients to the USIDNET registry that …

Humoral immunodeficiency and immune globulin replacement therapy (IGRT) usage in DiGeorge syndrome

SH Soshnick, T Joseph, NJ Bennett - Journal of Clinical Immunology, 2021 - Springer
USIDNET) registry previously described a discordance in the reported prevalence of humoral
immune deficiency in patients with DiGeorge syndromesyndrome in the USIDNET registry

Neutropenia is an underrecognized finding in pediatric primary immunodeficiency diseases: an analysis of the United States immunodeficiency network registry

TF Michniacki, JA Connelly, J Sturza… - Journal of Pediatric …, 2020 - journals.lww.com
… Neutropenia is more common in PIDD patients entered within the USIDNET registry than …
deficiency and others), and hyper-IgM syndrome; there was no statistically significant difference …

The hyper IgM syndromes: Epidemiology, pathogenesis, clinical manifestations, diagnosis and management

R Yazdani, S Fekrvand, S Shahkarami, G Azizi… - Clinical …, 2019 - Elsevier
Registry of the ESID on 56 affected males showed a 20% survival rate in individuals aged ~25
years [20]. The US X-HIGM Registry … third report of the national registry in Iran in 28 cases (…

Renal complications in patients with predominantly antibody deficiency in the United States Immune Deficiency Network (USIDNET)

…, D Suez, S Barmettler, USIDNET Consortium - Journal of Allergy and …, 2024 - Elsevier
… Our goal was to evaluate the prevalence and type of renal complications in patients with
PAD from the United States Immunodeficiency Network (USIDNET), a national registry of …

Autoimmune cytopenias and associated conditions in CVID: a report from the USIDNET registry

EJ Feuille, N Anooshiravani, KE Sullivan… - Journal of clinical …, 2018 - Springer
… Here, we report prevalence of autoimmune cytopenias in CVID from the USIDNET Registry
and compare the demographics and clinical features of patients with and without this …