West Syndrome: from etiology to prognosis

FMS Tomé - 2020 - estudogeral.uc.pt
The West syndrome is an epileptic encephalopathy in the child's first year of life, corresponding
to 1.4% of the epileptic syndromes in pediatric age. It is characterized by the triad: 1) …

Long-term weekly ACTH therapy for relapsed West syndrome in tuberous sclerosis complex: a case report

M Nakata, T Kato, M Ide, K Saito, T Yoshida… - Brain and …, 2016 - Elsevier
Relapse after initial ACTH therapy is a poor prognostic factor for long-term seizure control and
… Here, we report successful long-term weekly ACTH therapy for relapsed WS in a tuberous …

[PDF][PDF] Pattern of EEG change in infants with West syndrome: a retrospective study

K Fatema, MM Rahman, S Akhter, T Saad, N Akter… - Epilepsy …, 2018 - academia.edu
… of West syndrome who were followed up at least 6 months after diagnosis. We followed up
70 infants with West syndrome. … spasms for seizure relapse in patients with West syndrome. …

Everolimus in infants with tuberous sclerosis complex–related West syndrome: First results from a single‐center prospective observational study

S Samueli, A Dressler, G Gröppel, T Scholl… - Epilepsia, 2018 - Wiley Online Library
… There was no seizure relapse after initial response during the entire observation period.
At last observation, Patients 2 and 3 still were responders, and their EEGs showed focal …

An effective initial polytherapy for children with West syndrome

F Jia, H Jiang, L Du, N Li, J Sun… - Neural Regeneration …, 2013 - journals.lww.com
relapsed was treated with the polytherapy for a second time, and has thus far achieved
remission. The other two subjects who relapse … used to diagnose West syndrome: (1) seizures

[HTML][HTML] Cryptogenic West syndrome: Clinical profile, response to treatment and prognostic factors

MC Romero, EA Portillo, ML Lobato, BM Cabello… - Anales de Pediatría …, 2018 - Elsevier
… benign idiopathic forms in first- or second-degree relatives, and 2 had a personal history of
seizures prior to onset of spasms (neonatal seizures in one and febrile seizures in the other). …

The influence of etiology upon ictal semiology, treatment decisions and long-term outcomes in infantile spasms and West syndrome

AL Lux, JP Osborne - Epilepsy research, 2006 - Elsevier
… the West Delphi group. In the continual debate about whether we should “lump” or “split”
when studying epilepsy syndromes, … features of a seizure. This helps us to determine the likely …

Outcome for West syndrome following surgical treatment

BM Uthman, SA Reid, BJ Wilder, MR Andriola… - …, 1991 - Wiley Online Library
We report the case of an 18‐month‐old child with infantile spasms and a hypsarrhythmic
electroencephalogram (EEG) pattern associated with a porencephalic cyst. Surgical removal of …

Multicenter long‐term follow‐up of children with idiopathic West syndrome: ACTH versus vigabatrin

S Cohen‐Sadan, U Kramer, B Ben‐Zeev… - European Journal of …, 2009 - Wiley Online Library
… Categorical outcomes, such as presence or absence of relapse, and presence or absence
of cognitive impairment or seizures, were compared using Fisher’s exact test. A P-value of …

West Syndrome

JJ Millichap - Pellock's Pediatric Epilepsy: Diagnosis and …, 2016 - books.google.com
… Unfortunately, many infants with WS also develop focal seizures later or evolve into another
form of catastrophic epileptic encephalopathy, Lennox–Gastaut syndrome (7). Overall, a …