Abstract Dandy-Walker Syndrome (D-WS) is a rare disorder with an incidence of 1%–2% of
all central nervous system anomalies. The diagnosis can be challenging, especially in the
prenatal period. Here, we present an extremely rare case of D-WS associated with bilateral
congenital cataracts. A 36 weeks and 6 days old male baby presented with a Dandy-Walker
variant associated with bilateral congenital cataract. Ophthalmological examination revealed
microphthalmos and congenital cataracts present in both eyes with sclerocornea, iris …