… three major syndromes: an episodic vestibular syndrome, a progressive vestibular syndrome
and … include sensorineural hearing loss (SNHL) with a variable vestibular dysfunction [1, 2]. …

… familial aggregation and higher prevalence of vestibular syndromes in some ethnic groups
(4). However, the specifics of how genetic variations and familial clustering or aggregation …

… in common and rare vestibular diseases is starting to be … The genetic contribution to most
of the vestibular disorders is … vestibular syndromes, progressive vestibular syndrome, and …

… vestibular system and they represent a diagnostic challenge for the clinicians since their
genetic … This review will include syndromes with recurrent or episodic vertigo: familial episodic …

… progress in the discovery of genetic variants associated with vestibular disorders. We have
summarized molecular genetics finding in vestibular syndromes during the last 18 months. …

… distinct syndrome with autosomal dominance inheritance. NF1 occurs as a result of genetic
… In this review we discuss current knowledge of the genetics of VS. We focus on recent …

… Furthermore, the study of bilateral vestibulopathy may shed light on the pathophysiology of
more common vestibular syndromes such as benign recurrent vertigo and vestibular migraine…

… Between 1995 and 2012, over 100 causative genes have been identified for syndromic
and nonsyndromic forms of hereditary hearing loss. Mouse models have been extremely …

… with syndromic and non-syndromic genetic HL undergoing vestibular evaluation prior to
cochlear implantation. Improved understanding of the molecular physiology of vestibular hair …

… Attempts at linkage mapping by various groups concur that there is genetic heterogeneity,
which is not unexpected, as is the case for inherited deafness syndromes. Initial analysis …