… of bronchiectasis, and correlates with lung function … of particular interest for CF lung disease
but must be carefully studied … the pathogenesis of CF lung disease, summarizes the results …

… Progressive lung disease in cystic fibrosis (CF) is the life-limiting factor of this autosomal …
of CF lung disease, hence longitudinal imaging is recommended for disease monitoring in the …

… of new therapeutics to treat bronchiectasis in cystic fibrosis can be maintained … lung function,
and evidence suggests that such endpoints are less responsive in the adult cystic fibrosis …

… Lung explant tissue from three adult patients with CF with end-stage CF lung disease was
used for development of the staining protocols and the double-staining experiments. Details of …

… with their non-cystic fibrosis littermate controls.24 The … of cystic fibrosis lung disease in
humans. These studies suggest an increased predisposition to lung disease in the cystic fibrosis …

… TGFβ1 as a likely modifier in another disease of the lung (ie, cystic fibrosis). … lung disease
in animal models and humans, including disease progression in idiopathic pulmonary fibrosis, …

… who carried the A455E mutation had significantly better lung function … lung disease. To
investigate this possibility, we compared clinical data from a group of patients with cystic fibrosis …

… of cystic fibrosis (CF) lung disease is poorly correlated with CFTR mutation. Although
numerous candidates have been investigated, the role for modifier genes in CF lung disease …

… of cystic fibrosis-related diabetes mellitus is tightly linked to poor lung function in patients
with cystic fibrosis: data from the European Epidemiologic Registry of Cystic Fibrosis. Pediatr …

… contributes independently to lung disease and constitutes an … The Cystic Fibrosis Foundation
center network provides not … can relegate the lung disease of CF to an historical curiosity. …